{"id":15908,"date":"2020-11-22T13:57:37","date_gmt":"2020-11-22T13:57:37","guid":{"rendered":"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/"},"modified":"2026-03-10T16:46:43","modified_gmt":"2026-03-10T16:46:43","slug":"pilomatrix-carcinoom","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/nl\/carcinoma-de-pilomatriz\/","title":{"rendered":"Carcinoma de pilomatriz"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Entendiendo el Carcinoma de Pilomatriz: Definici\u00f3n y Caracter\u00edsticas<\/h1>\n<p>El carcinoma de pilomatriz representa una forma <span class=\"term\" data-term-id=\"176\">maligna<\/span> rara que emerge a partir de un pilomatricoma previamente <span class=\"term\" data-term-id=\"22\">benigno<\/span>, origin\u00e1ndose en el <span style=\"font-weight: bold;\" data-term-id=\"1300\">fol\u00edculo piloso<\/span> o <span style=\"font-weight: bold;\" data-term-id=\"122\">capello<\/span>. No fue sino hasta el a\u00f1o 1980 que una evaluaci\u00f3n exhaustiva de varios casos de pilomatricomas con comportamiento biol\u00f3gicamente agresivo logr\u00f3 confirmar la transformaci\u00f3n maligna de estos tumores, habitualmente no cancerosos. Desde esa confirmaci\u00f3n, escasamente se han reportado 90 casos de este carcinoma. Es relevante notar que algunos desarrollos de carcinoma pilomatrix han aparecido como una <span class=\"term\" data-term-id=\"164\">lesi\u00f3n<\/span> <span class=\"term\" data-term-id=\"746\">de novo<\/span>. El riesgo de <span class=\"term\" data-term-id=\"1074\">reaparici\u00f3n<\/span> tras una cirug\u00eda de <span class=\"term\" data-term-id=\"848\">excisi\u00f3n<\/span> es considerable, y las caracter\u00edsticas malignas frecuentemente se observan en <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> <span class=\"term\" data-term-id=\"805\">recurrentes<\/span>.<\/p>\n<p>Este tumor tambi\u00e9n es conocido por otros nombres, incluyendo pilomatricarcinoma y carcinoma pilom\u00e1trico.<\/p>\n<h2>Manifestaciones Cl\u00ednicas Distintivas del Carcinoma de Pilomatrix<\/h2>\n<p>Generalmente, las lesiones de carcinoma de pilomatriz se localizan en la regi\u00f3n de la cabeza y el cuello, exhibiendo un rango de tama\u00f1o entre 1 cm y 10 cm. A diferencia de su contraparte benigna, que afecta m\u00e1s a menudo a ni\u00f1os peque\u00f1os de ambos <span class=\"term\" data-term-id=\"1167\">sexos<\/span>, la variante maligna muestra una predilecci\u00f3n al doble de frecuencia por hombres blancos de edad media.<\/p>\n<p>Se ha documentado la presencia de <span class=\"term\" data-term-id=\"383\">met\u00e1stasis<\/span> hacia el pulm\u00f3n, un evento que puede suscitarse a\u00f1os despu\u00e9s del diagn\u00f3stico primario.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>M\u00e9todos de Diagn\u00f3stico para el Carcinoma de Pilomatriz<\/h2>\n<p>La identificaci\u00f3n definitiva del carcinoma de pilomatriz se establece mediante el an\u00e1lisis <span class=\"term\" data-term-id=\"474\">histol\u00f3gico<\/span> de una muestra obtenida mediante una <span class=\"term\" data-term-id=\"24\">biopsia<\/span> cut\u00e1nea. Aunque existen similitudes histol\u00f3gicas con el pilomatricoma benigno, el diagn\u00f3stico maligno se refuerza por la presencia de las siguientes caracter\u00edsticas adicionales:<\/p>\n<ul>\n<li>Presencia frecuente de <span class=\"term\" data-term-id=\"1534\">mitosis<\/span> anormales.<\/li>\n<li><span class=\"term\" data-term-id=\"403\">Necrosis<\/span> localizada en el centro de la lesi\u00f3n o dentro del tumor.<\/li>\n<li>Capacidad de <span class=\"term\" data-term-id=\"543\">infiltraci\u00f3n<\/span> en la piel circundante y el <span class=\"term\" data-term-id=\"1183\">tejido suave<\/span> subyacente.<\/li>\n<li>Infiltraci\u00f3n hacia el sistema circulatorio sangu\u00edneo y <span class=\"term\" data-term-id=\"744\">linf\u00e1tico<\/span>.<\/li>\n<\/ul>\n<p>Podr\u00eda requerirse una <span class=\"term\" data-term-id=\"1116\">resonancia magn\u00e9tica<\/span> (imagen por <span class=\"term\" data-term-id=\"1410\">resonancia magn\u00e9tica<\/span>) para evaluar la extensi\u00f3n local del <span class=\"term\" data-term-id=\"289\">tumor<\/span>. Adicionalmente, la <span class=\"term\" data-term-id=\"2176\">palpaci\u00f3n<\/span> de los <span class=\"term\" data-term-id=\"2123\">linfa<\/span> <span class=\"term\" data-term-id=\"1775\">nodos<\/span> y una exploraci\u00f3n mediante <span class=\"term\" data-term-id=\"799\">TC<\/span> (Tomograf\u00eda Computarizada) pueden realizarse para descartar la presencia de met\u00e1stasis en \u00f3rganos como los pulmones y el h\u00edgado.<\/p>\n<h2>Opciones de Tratamiento Eficaces para el Carcinoma Pilomatrix<\/h2>\n<p>Dada la capacidad del tumor para generar <span class=\"term\" data-term-id=\"185\">met\u00e1stasis<\/span> en diversas ubicaciones, el tratamiento de elecci\u00f3n es la excisi\u00f3n quir\u00fargica completa con m\u00e1rgenes de seguridad amplios (de 2 a 3 cm). La Cirug\u00eda Microgr\u00e1fica de Mohs puede ser empleada estrat\u00e9gicamente para lograr un mejor <span class=\"term\" data-term-id=\"1854\">control<\/span> del margen quir\u00fargico. Se ha observado que las resecciones incompletas conducen sistem\u00e1ticamente a recurrencias locales.<\/p>\n<p>Tambi\u00e9n se ha explorado la <span class=\"term\" data-term-id=\"1325\">radioterapia<\/span> <span class=\"term\" data-term-id=\"1073\">auxiliar<\/span> como tratamiento complementario, aunque su eficacia y beneficios claros a\u00fan no est\u00e1n completamente establecidos por la evidencia cl\u00ednica.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Entendiendo el Carcinoma de Pilomatriz: Definici\u00f3n y Caracter\u00edsticas El carcinoma de pilomatriz representa una forma maligna rara que emerge a partir de un pilomatricoma previamente benigno, origin\u00e1ndose en el fol\u00edculo piloso o capello. No fue sino hasta el a\u00f1o 1980 que una evaluaci\u00f3n exhaustiva de varios casos de pilomatricomas con comportamiento biol\u00f3gicamente agresivo logr\u00f3 confirmar [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"template":"","glossary-cat":[],"class_list":["post-15908","glossary","type-glossary","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Carcinoma de pilomatriz - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/nl\/pilomatrix-carcinoom\/\" \/>\n<meta property=\"og:locale\" content=\"nl_NL\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Carcinoma de pilomatriz\" \/>\n<meta property=\"og:description\" content=\"Entendiendo el Carcinoma de Pilomatriz: Definici\u00f3n y Caracter\u00edsticas El carcinoma de pilomatriz representa una forma maligna rara que emerge a partir de un pilomatricoma previamente benigno, origin\u00e1ndose en el fol\u00edculo piloso o capello. No fue sino hasta el a\u00f1o 1980 que una evaluaci\u00f3n exhaustiva de varios casos de pilomatricomas con comportamiento biol\u00f3gicamente agresivo logr\u00f3 confirmar [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/dermatly.com\/nl\/pilomatrix-carcinoom\/\" \/>\n<meta property=\"og:site_name\" content=\"Dermatly.com - El sitio de tu piel\" \/>\n<meta property=\"article:modified_time\" content=\"2026-03-10T16:46:43+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Geschatte leestijd\" \/>\n\t<meta name=\"twitter:data1\" content=\"2 minuten\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/\",\"url\":\"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/\",\"name\":\"Carcinoma de pilomatriz - Dermatly.com - El sitio de tu piel\",\"isPartOf\":{\"@id\":\"https:\/\/dermatly.com\/#website\"},\"datePublished\":\"2020-11-22T13:57:37+00:00\",\"dateModified\":\"2026-03-10T16:46:43+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/#breadcrumb\"},\"inLanguage\":\"nl-NL\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/dermatly.com\/carcinoma-de-pilomatriz\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/dermatly.com\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Glossary\",\"item\":\"https:\/\/dermatly.com\/glossary\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Carcinoma de pilomatriz\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/dermatly.com\/#website\",\"url\":\"https:\/\/dermatly.com\/\",\"name\":\"Dermatly.com - El sitio de tu piel\",\"description\":\"Dermatolog\u00eda y lesiones de la piel\",\"publisher\":{\"@id\":\"https:\/\/dermatly.com\/#organization\"},\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/dermatly.com\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"nl-NL\"},{\"@type\":\"Organization\",\"@id\":\"https:\/\/dermatly.com\/#organization\",\"name\":\"dermatly.com\",\"url\":\"https:\/\/dermatly.com\/\",\"logo\":{\"@type\":\"ImageObject\",\"inLanguage\":\"nl-NL\",\"@id\":\"https:\/\/dermatly.com\/#\/schema\/logo\/image\/\",\"url\":\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/dermatly-logo.png\",\"contentUrl\":\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/dermatly-logo.png\",\"width\":448,\"height\":110,\"caption\":\"dermatly.com\"},\"image\":{\"@id\":\"https:\/\/dermatly.com\/#\/schema\/logo\/image\/\"}}]}<\/script>\n<!-- \/ Yoast SEO Premium plugin. -->","yoast_head_json":{"title":"Carcinoma de pilomatriz - Dermatly.com - El sitio de tu piel","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/dermatly.com\/nl\/pilomatrix-carcinoom\/","og_locale":"nl_NL","og_type":"article","og_title":"Carcinoma de pilomatriz","og_description":"Entendiendo el Carcinoma de Pilomatriz: Definici\u00f3n y Caracter\u00edsticas El carcinoma de pilomatriz representa una forma maligna rara que emerge a partir de un pilomatricoma previamente benigno, origin\u00e1ndose en el fol\u00edculo piloso o capello. 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