{"id":15323,"date":"2020-11-22T03:57:07","date_gmt":"2020-11-22T03:57:07","guid":{"rendered":"https:\/\/dermatly.com\/patologia-de-la-pitiriasis-rubra-pilaris\/"},"modified":"2026-03-10T16:31:49","modified_gmt":"2026-03-10T16:31:49","slug":"pathologie-van-pityriasis-rubra-pilaris","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/nl\/patologia-de-la-pitiriasis-rubra-pilaris\/","title":{"rendered":"Pathologie van Pityriasis Rubra Pilaris"},"content":{"rendered":"<section class=\"textBlock\">\n<p>La <span class=\"term\" data-term-id=\"234\">Pitiriasis rubra pilaris<\/span> (PRP) se manifiesta cl\u00ednicamente como una <span class=\"term\" data-term-id=\"1476\">erupci\u00f3n papuloescamosa<\/span> caracterizada por taponamiento <span class=\"term\" data-term-id=\"107\">folicular<\/span> y <span class=\"term\" data-term-id=\"90\">eritema<\/span> <span class=\"term\" data-term-id=\"316\">perifolicular<\/span>. Todas las presentaciones cl\u00ednicas comparten los mismos fundamentos histopatol\u00f3gicos.<\/p>\n<h1>Histopatolog\u00eda de la Pitiriasis Rubra Pilaris<\/h1>\n<p>En la PRP, el <span class=\"term\" data-term-id=\"85\">epidermis<\/span> exhibe una <span class=\"term\" data-term-id=\"2\">acantosis<\/span> regular junto con <span class=\"term\" data-term-id=\"136\">hiperplasia<\/span> de patr\u00f3n <span class=\"term\" data-term-id=\"248\"><span class=\"term\" data-term-id=\"1902\">psoriasiforme<\/span><\/span> (observar figuras 1-3). La capa <span class=\"term\" data-term-id=\"130\">c\u00f3rnea<\/span> se engrosa, presentando focos <span class=\"term\" data-term-id=\"1337\">paraquerat\u00f3sicos<\/span> intercalados con \u00e1reas de <span class=\"term\" data-term-id=\"211\">ortoqueratosis<\/span>, tanto en orientaci\u00f3n vertical como horizontal (aunque esto \u00faltimo no se aprecia claramente en las im\u00e1genes suministradas). La <span class=\"term\" data-term-id=\"610\">hiperqueratosis<\/span> se extiende hacia las aberturas de las estructuras foliculares, creando tapones foliculares prominentes (figuras 1-3). En menor medida, el <span class=\"term\" data-term-id=\"61\">dermis<\/span> puede mostrar un <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> <span class=\"term\" data-term-id=\"168\">liquenoide<\/span> mezclado. Es infrecuente, pero se pueden observar focos de <span class=\"term\" data-term-id=\"3\">acant\u00f3lisis<\/span> (figura 3), lo que ha llevado a algunos especialistas a establecer correlaciones con la enfermedad de Darier.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h2 class=\"colour--primary\">Patolog\u00eda Dermatosc\u00f3pica de la Pitiriasis Rubra Pilaris<\/h2>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/prp-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microscop\u00eda mostrando la histopatolog\u00eda de la Pitiriasis Rubra Pilaris, Figura 1.\"><\/div>\n<p class=\"p-small\">Figura 1<\/p>\n<\/p><\/div>\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/prp-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microscop\u00eda mostrando la histopatolog\u00eda de la Pitiriasis Rubra Pilaris, Figura 2.\"><\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<\/p><\/div>\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/prp-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microscop\u00eda mostrando la histopatolog\u00eda de la Pitiriasis Rubra Pilaris, Figura 3, con posible acant\u00f3lisis.\"><\/div>\n<p class=\"p-small\">figura 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>Estudios Complementarios en la Pitiriasis Rubra Pilaris<\/h2>\n<p>Generalmente, no se requiere la realizaci\u00f3n de estudios complementarios para el diagn\u00f3stico. No obstante, la tinci\u00f3n PAS puede ser valiosa para excluir la presencia de <span class=\"term\" data-term-id=\"2101\">infecciones<\/span> f\u00fangicas asociadas.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>Diagn\u00f3stico Diferencial de la Pitiriasis Rubra Pilaris<\/h2>\n<p><strong>Psoriasis:<\/strong> La presencia de <span class=\"term\" data-term-id=\"542\">infiltrados<\/span> <span class=\"term\" data-term-id=\"443\">neutrof\u00edlicos<\/span> y la pustulaci\u00f3n espongiforme apuntan m\u00e1s fuertemente hacia la psoriasis.<\/p>\n<p><strong>S\u00edfilis Secundaria:<\/strong> Este padecimiento debe considerarse en el diagn\u00f3stico diferencial debido a sus <span class=\"term\" data-term-id=\"1015\">erupciones<\/span> de patr\u00f3n psoriasiforme, caracter\u00edsticas liquenoides y la presencia de <span class=\"term\" data-term-id=\"1513\">c\u00e9lulas plasm\u00e1ticas<\/span> en la biopsia.<\/p>\n<p><strong>Micosis Fungoide:<\/strong> Un patr\u00f3n mixto de <span class=\"term\" data-term-id=\"528\">espongiosis<\/span> psoriasiforme junto con hallazgos liquenoides obliga a plantear la posibilidad de micosis fungoide o parapsoriasis subyacente. La identificaci\u00f3n precisa de estos espectros es crucial para un manejo terap\u00e9utico adecuado.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>La Pitiriasis rubra pilaris (PRP) se manifiesta cl\u00ednicamente como una erupci\u00f3n papuloescamosa caracterizada por taponamiento folicular y eritema perifolicular. Todas las presentaciones cl\u00ednicas comparten los mismos fundamentos histopatol\u00f3gicos. Histopatolog\u00eda de la Pitiriasis Rubra Pilaris En la PRP, el epidermis exhibe una acantosis regular junto con hiperplasia de patr\u00f3n psoriasiforme (observar figuras 1-3). La capa c\u00f3rnea [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":15327,"parent":0,"template":"","glossary-cat":[],"class_list":["post-15323","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda de la pitiriasis rubra pilaris - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/nl\/pathologie-van-pityriasis-rubra-pilaris\/\" \/>\n<meta property=\"og:locale\" content=\"nl_NL\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda de la pitiriasis rubra pilaris\" \/>\n<meta property=\"og:description\" content=\"La Pitiriasis rubra pilaris (PRP) se manifiesta cl\u00ednicamente como una erupci\u00f3n papuloescamosa caracterizada por taponamiento folicular y eritema perifolicular. Todas las presentaciones cl\u00ednicas comparten los mismos fundamentos histopatol\u00f3gicos. Histopatolog\u00eda de la Pitiriasis Rubra Pilaris En la PRP, el epidermis exhibe una acantosis regular junto con hiperplasia de patr\u00f3n psoriasiforme (observar figuras 1-3). 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