{"id":4574,"date":"2020-11-11T13:38:11","date_gmt":"2020-11-11T13:38:11","guid":{"rendered":"https:\/\/dermatly.com\/telangiectasia-benigna-hereditaria\/"},"modified":"2026-03-10T10:10:33","modified_gmt":"2026-03-10T10:10:33","slug":"teleangectasia-benigna-ereditaria","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/it\/telangiectasia-benigna-hereditaria\/","title":{"rendered":"Teleangectasia ereditaria benigna"},"content":{"rendered":"<section class=\"textBlock\">\n<h2>Que es <span class=\"term\" data-term-id=\"281\">telangiectasia<\/span>?<\/h2>\n<p>El t\u00e9rmino telangiectasia se refiere a una afecci\u00f3n cut\u00e1nea compuesta por una fina <span class=\"term\" data-term-id=\"953\">vasos sanguineos<\/span>: estos se llaman <span class=\"term\" data-term-id=\"700\">telangiectasias<\/span>.<\/p>\n<p><span class=\"term\" data-term-id=\"47\">Cut\u00e1neo<\/span> Las telangiectasias son causadas por la dilataci\u00f3n permanente de peque\u00f1os vasos sangu\u00edneos que resultan en peque\u00f1os vasos rojos <span class=\"term\" data-term-id=\"321\">lineal<\/span> marcas en la piel y <span class=\"term\" data-term-id=\"188\">mucoso<\/span> membranas.  Ellos pueden ser <span class=\"term\" data-term-id=\"949\">primario<\/span> o secundaria.<\/p>\n<ul>\n<li>Las telangiectasias primarias son causadas por <span class=\"term\" data-term-id=\"862\">idiop\u00e1tico<\/span> <span class=\"term\" data-term-id=\"756\">capilar<\/span> dilataci\u00f3n (causa desconocida).<\/li>\n<li>Las telangiectasias secundarias se producen como una caracter\u00edstica de una enfermedad cut\u00e1nea o <span class=\"term\" data-term-id=\"380\">sist\u00e9mico<\/span> proceso de la enfermedad.<\/li>\n<\/ul>\n<h2>Que es <span class=\"term\" data-term-id=\"22\">benigno<\/span> <span class=\"term\" data-term-id=\"1745\">hereditario<\/span> telangiectasia?<\/h2>\n<p>La telangiectasia hereditaria benigna es una <span class=\"term\" data-term-id=\"2281\">telangiect\u00e1sico<\/span> trastorno.  Tiene diferentes patrones cl\u00ednicos.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                        <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p><script>\n    if (ads_screenwidth < 780 ) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-8';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-8');\n            });\n        })();\n    }\n<\/script>\n                    <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>\u00bfQu\u00e9 causa la telangiectasia hereditaria benigna y qui\u00e9n est\u00e1 en riesgo?<\/h2>\n<p>Se desconoce la causa precisa de la telangiectasia hereditaria benigna.<\/p>\n<ul>\n<li>Se hereda en un <span class=\"term\" data-term-id=\"828\">autos\u00f3mico<\/span> patr\u00f3n dominante.  Esto significa que se transmite de uno de los padres a aproximadamente la mitad de sus hijos, por lo que varios miembros de la familia pueden verse afectados.<\/li>\n<li>Las telangiectasias tienden a aparecer en los primeros a\u00f1os de vida, a menudo entre los 2 y los 12 a\u00f1os.  Rara vez est\u00e1n presentes al nacer.<\/li>\n<li>Las mujeres suelen notar m\u00e1s las telangiectasias, pero no se cree que el trastorno sea m\u00e1s com\u00fan en las mujeres.<\/li>\n<li>Las telangiectasias tambi\u00e9n pueden volverse m\u00e1s prominentes durante el embarazo.<\/li>\n<li>A menudo se distribuyen en sitios expuestos a la luz, lo que implica que la luz solar puede desempe\u00f1ar un papel.<\/li>\n<\/ul>\n<h2>\u00bfCu\u00e1les son las caracter\u00edsticas cl\u00ednicas de la telangiectasia hereditaria benigna?<\/h2>\n<p>Los individuos con telangiectasia hereditaria benigna tienden a presentar numerosas telangiectasias.<\/p>\n<ul>\n<li>A menudo se distribuyen ampliamente por la cara, el cuello, la parte superior del tronco, <span class=\"term\" data-term-id=\"71\">dorsal<\/span>, manos y, con menor frecuencia, rodillas.<\/li>\n<li>Las telangiectasias pueden ser <span class=\"term\" data-term-id=\"1063\">macular<\/span>, <span class=\"term\" data-term-id=\"235\">placa<\/span>-como, arborizaci\u00f3n, <span class=\"term\" data-term-id=\"1343\">reticular<\/span>, <span class=\"term\" data-term-id=\"2397\">puntuar<\/span>, moteado, en forma de ara\u00f1a y lineal.<\/li>\n<li>Las telangiectasias punteadas pueden estar rodeadas de halos p\u00e1lidos (fen\u00f3meno de robo).<\/li>\n<li>Algunos <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> puede ser indistinguible de la ara\u00f1a <span class=\"term\" data-term-id=\"699\">telangiectasia<\/span>.<\/li>\n<li>Las telangiectasias tempranas pueden ser peque\u00f1as y <span class=\"term\" data-term-id=\"967\">eritematoso<\/span>.  A menudo aumentan de tama\u00f1o y pueden volverse m\u00e1s p\u00e1lidos con la edad.<\/li>\n<li>los <span class=\"term\" data-term-id=\"1018\">mucosa<\/span> las membranas no se ven afectadas a excepci\u00f3n del borde bermell\u00f3n de los labios.<\/li>\n<li>No hay afectaci\u00f3n sist\u00e9mica ni hemorragia, a diferencia de la hereditaria. <span class=\"term\" data-term-id=\"121\">hemorr\u00e1gico<\/span> telangiectasia.<\/li>\n<li>Las telangiectasias son invariablemente <span class=\"term\" data-term-id=\"731\">asintom\u00e1tico<\/span> y s\u00f3lo causan una leve preocupaci\u00f3n cosm\u00e9tica.<\/li>\n<\/ul>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h5 class=\"colour--primary\">Telangiectasia hereditaria benigna<\/h5>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-01__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-02__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-03__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-04__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-05__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-06__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-07__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/benign-telangiectasia-08__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Telangiectasia hereditaria benigna\"><\/div>\n<p class=\"p-small\">Telangiectasia hereditaria benigna<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>\u00bfC\u00f3mo se diagnostica la telangiectasia hereditaria benigna?<\/h2>\n<p>La telangiectasia hereditaria benigna es un diagn\u00f3stico cl\u00ednico. <span class=\"term\" data-term-id=\"474\">Histol\u00f3gico<\/span> examen de <span class=\"term\" data-term-id=\"2114\">lesional<\/span> la piel muestra dilataci\u00f3n del subpapilar <span class=\"term\" data-term-id=\"1178\">venoso<\/span> <span class=\"term\" data-term-id=\"2213\">plexo<\/span> con parte superior asociada <span class=\"term\" data-term-id=\"52\">d\u00e9rmico<\/span> <span class=\"term\" data-term-id=\"18\">atrofia<\/span>.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                        <!-- \/340621630\/dermnet_mobile_after4sections_300x250' --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-9\" class=\"[ js-hideable ]\"><\/div>\n<p><script>\n    if (ads_screenwidth < 780 ) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-9';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-9\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-9');\n            });\n        })();\n    }\n<\/script>\n                    <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>\u00bfCu\u00e1les son los diagn\u00f3sticos diferenciales de las telangiectasias?<\/h2>\n<p>La condici\u00f3n m\u00e1s importante a descartar es la telangiectasia hemorr\u00e1gica hereditaria (Osler-Rendu-Weber <span class=\"term\" data-term-id=\"350\">s\u00edndrome<\/span>).  Los diagn\u00f3sticos diferenciales de telangiectasias primarias en ni\u00f1os tambi\u00e9n incluyen:<\/p>\n<ul>\n<li>Telangiectasia de ara\u00f1a<\/li>\n<li>  Ataxia-telangiectasia <\/li>\n<li><span class=\"term\" data-term-id=\"308\">Generalizado<\/span> telangiectasia esencial<\/li>\n<li><span class=\"term\" data-term-id=\"292\">Unilateral<\/span> telangiectasia nevoide<\/li>\n<li> <span class=\"term\" data-term-id=\"358\">Angioma<\/span> serpiginoso <\/li>\n<li>Capilar <span class=\"term\" data-term-id=\"753\">vascular<\/span> <span class=\"term\" data-term-id=\"2129\">malformaciones<\/span><\/li>\n<\/ul>\n<h2>\u00bfCu\u00e1l es el tratamiento y el resultado de la telangiectasia hereditaria benigna?<\/h2>\n<p>Debido a la falta de afectaci\u00f3n sist\u00e9mica, la telangiectasia hereditaria benigna tiene una excelente <span class=\"term\" data-term-id=\"241\">pron\u00f3stico<\/span> y generalmente no se requiere intervenci\u00f3n m\u00e9dica.<\/p>\n<p>Cuando se solicita un tratamiento por razones est\u00e9ticas, se pueden considerar los siguientes tratamientos.<\/p>\n<ul>\n<li>Escleroterapia<\/li>\n<li>  Luz pulsada intensa <\/li>\n<li>Vascular <span class=\"term\" data-term-id=\"1617\">l\u00e1ser<\/span> <\/li>\n<li>  Electrocirug\u00eda <\/li>\n<\/ul>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Que es telangiectasia? El t\u00e9rmino telangiectasia se refiere a una afecci\u00f3n cut\u00e1nea compuesta por una fina vasos sanguineos: estos se llaman telangiectasias. Cut\u00e1neo Las telangiectasias son causadas por la dilataci\u00f3n permanente de peque\u00f1os vasos sangu\u00edneos que resultan en peque\u00f1os vasos rojos lineal marcas en la piel y mucoso membranas. Ellos pueden ser primario o secundaria. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":4583,"parent":0,"template":"","glossary-cat":[],"class_list":["post-4574","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Telangiectasia benigna hereditaria - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/it\/teleangectasia-benigna-ereditaria\/\" \/>\n<meta property=\"og:locale\" content=\"it_IT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Telangiectasia benigna hereditaria\" \/>\n<meta property=\"og:description\" content=\"Que es telangiectasia? El t\u00e9rmino telangiectasia se refiere a una afecci\u00f3n cut\u00e1nea compuesta por una fina vasos sanguineos: estos se llaman telangiectasias. Cut\u00e1neo Las telangiectasias son causadas por la dilataci\u00f3n permanente de peque\u00f1os vasos sangu\u00edneos que resultan en peque\u00f1os vasos rojos lineal marcas en la piel y mucoso membranas. Ellos pueden ser primario o secundaria. 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