{"id":2818,"date":"2020-11-08T12:34:13","date_gmt":"2020-11-08T12:34:13","guid":{"rendered":"https:\/\/dermatly.com\/linfoma-extraganglionar-de-celulas-nk-t-tipo-nasal-patologia\/"},"modified":"2026-03-10T14:37:44","modified_gmt":"2026-03-10T14:37:44","slug":"patologia-nasale-di-tipo-nk-t-linfoma-extranodale","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/it\/linfoma-extraganglionar-de-celulas-nk-t-tipo-nasal-patologia\/","title":{"rendered":"Linfoma extranodale a cellule NK\/T, tipo nasale, patologia"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Linfoma Extranodal de C\u00e9lulas NK\/T, Tipo Nasal: Caracter\u00edsticas y Patolog\u00eda<\/h1>\n<p>El <span class=\"term\" data-term-id=\"1790\">Linfoma Extranodal<\/span> NK\/T, tipo nasal, es una neoplasia impulsada por el virus de Epstein-Barr (VEB). Habitualmente, esta afecci\u00f3n compromete primariamente el tracto respiratorio superior (v\u00e9ase tambi\u00e9n Trastornos <span class=\"term\" data-term-id=\"1402\">linfoproliferativos<\/span> asociados al VEB). Aunque la afectaci\u00f3n cut\u00e1nea suele ser secundaria, en algunos casos la enfermedad puede manifestarse predominantemente en la piel.<\/p>\n<h2>Histolog\u00eda del Linfoma Extranodal de C\u00e9lulas NK\/T, Tipo Nasal<\/h2>\n<p>En el Linfoma Extranodal de C\u00e9lulas NK\/T, tipo nasal, la histopatolog\u00eda t\u00edpicamente revela un denso <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> <span class=\"term\" data-term-id=\"52\">d\u00e9rmico<\/span>, el cual frecuentemente se extiende hacia el tejido <span class=\"term\" data-term-id=\"1282\">subcut\u00e1neo<\/span> (Figura 1). Es com\u00fan observar <span class=\"term\" data-term-id=\"96\">exocitosis<\/span> de <span class=\"term\" data-term-id=\"421\">linfocitos<\/span> <span class=\"term\" data-term-id=\"1395\">at\u00edpicos<\/span> dentro del <span class=\"term\" data-term-id=\"85\">epidermis<\/span>, una caracter\u00edstica que puede simular estrechamente la micosis fungoide (Figura 2).<\/p>\n<p>El <span class=\"term\" data-term-id=\"61\">dermis<\/span> est\u00e1 ocupado por un infiltrado generalmente <span class=\"term\" data-term-id=\"1064\">polimorfo<\/span>, que puede contener numerosos <span class=\"term\" data-term-id=\"858\">histiocitos<\/span> y <span class=\"term\" data-term-id=\"448\">eosin\u00f3filos<\/span>. Las c\u00e9lulas malignas var\u00edan en tama\u00f1o, desde peque\u00f1as hasta medianas, con algunas formas m\u00e1s grandes presentes (Figuras 3 y 4). Es frecuente que el infiltrado involucre las paredes vasculares (Figuras 3 y 4), provocando <span class=\"term\" data-term-id=\"753\">vascular<\/span> y restos <span class=\"term\" data-term-id=\"1612\">nucleares<\/span> (observables focalmente en la Figura 4). Otro hallazgo patol\u00f3gico recurrente es la presencia de <span class=\"term\" data-term-id=\"403\">necrosis<\/span>.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h2 class=\"colour--primary\">Im\u00e1genes de la Patolog\u00eda del Linfoma Extranodal de C\u00e9lulas NK\/T, Tipo Nasal<\/h2>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/nktcell-fig-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Histopatolog\u00eda que muestra un denso infiltrado d\u00e9rmico caracter\u00edstico del Linfoma Extranodal de C\u00e9lulas NK\/T, tipo nasal.\"><\/p>\n<p class=\"p-small\">Figura 1<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/nktcell-fig-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Exocitosis de linfocitos at\u00edpicos en la epidermis, similar a la micosis fungoide en el Linfoma Extranodal de C\u00e9lulas NK\/T, tipo nasal.\"><\/p>\n<p class=\"p-small\">Figura 2<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/nktcell-fig-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Infiltrado linfomatoso afectando las paredes vasculares en el Linfoma Extranodal de C\u00e9lulas NK\/T.\"><\/p>\n<p class=\"p-small\">Figura 3<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/nktcell-fig-4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Observaci\u00f3n de afectaci\u00f3n vascular con restos nucleares en el contexto del Linfoma Extranodal de C\u00e9lulas NK\/T.\"><\/p>\n<p class=\"p-small\">Figura 4<\/p>\n<\/p><\/div>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<p>Comprender las caracter\u00edsticas histopatol\u00f3gicas es fundamental para el diagn\u00f3stico diferencial de las infiltraciones cut\u00e1neas at\u00edpicas asociadas al VEB. La apariencia polimorfa y la afectaci\u00f3n vascular son claves para distinguir este linfoma de otras entidades linfoproliferativas.<\/p>\n<\/section>\n<div class=\"ad-container\">\n                    <script>\n    if (window.innerWidth < 780) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-8';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-8');\n            });\n        })();\n    }\n<\/script>\n                <\/div>\n<h1>An\u00e1lisis Especializado para el Linfoma Extranodal NK\/T de Tipo Nasal<\/h1>\n<p>La realizaci\u00f3n de tinciones especiales es un paso crucial para establecer el diagn\u00f3stico definitivo. En el sitio de la lesi\u00f3n, la hibridaci\u00f3n in situ con t\u00e9cnicas para el virus de Epstein-Barr (EBV) revela positividad en las c\u00e9lulas at\u00edpicas. Generalmente, estas c\u00e9lulas muestran positividad inmunohistoqu\u00edmica para marcadores como CD56 y granzima o TIA1. Mientras que algunos casos pueden expresar el marcador de c\u00e9lulas T, CD3, los estudios de reordenamiento gen\u00e9tico de c\u00e9lulas T suelen arrojar resultados negativos.<\/p>\n<h2>Consideraciones Diagn\u00f3sticas Diferenciales del Linfoma Extranodal NK\/T de Tipo Nasal<\/h2>\n<p>Otros linfomas de c\u00e9lulas T perif\u00e9ricos y la paniculitis linfomatosa similar a c\u00e9lulas T subcut\u00e1neas pueden presentar caracter\u00edsticas morfol\u00f3gicas que se asemejan a este tipo de linfoma. Si los resultados de los estudios de reordenamiento de genes de c\u00e9lulas T son positivos, junto con una inmunohistoqu\u00edmica de c\u00e9lulas T positiva, esto favorecer\u00eda el diagn\u00f3stico de un linfoma de c\u00e9lulas T genuino. La coexistencia de positividad para EBV, CD56 y granzima en un contexto de malignidad linfoide es un hallazgo infrecuente en la mayor\u00eda de los otros linfomas de c\u00e9lulas T, ayudando a delimitar el diagn\u00f3stico hacia el subtipo NK\/T.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Linfoma Extranodal de C\u00e9lulas NK\/T, Tipo Nasal: Caracter\u00edsticas y Patolog\u00eda El Linfoma Extranodal NK\/T, tipo nasal, es una neoplasia impulsada por el virus de Epstein-Barr (VEB). Habitualmente, esta afecci\u00f3n compromete primariamente el tracto respiratorio superior (v\u00e9ase tambi\u00e9n Trastornos linfoproliferativos asociados al VEB). Aunque la afectaci\u00f3n cut\u00e1nea suele ser secundaria, en algunos casos la enfermedad puede [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":2823,"parent":0,"template":"","glossary-cat":[],"class_list":["post-2818","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Linfoma extraganglionar de c\u00e9lulas NK \/ T, tipo nasal, patolog\u00eda - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/it\/patologia-nasale-di-tipo-nk-t-linfoma-extranodale\/\" \/>\n<meta property=\"og:locale\" content=\"it_IT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Linfoma extraganglionar de c\u00e9lulas NK \/ T, tipo nasal, patolog\u00eda\" \/>\n<meta property=\"og:description\" content=\"Linfoma Extranodal de C\u00e9lulas NK\/T, Tipo Nasal: Caracter\u00edsticas y Patolog\u00eda El Linfoma Extranodal NK\/T, tipo nasal, es una neoplasia impulsada por el virus de Epstein-Barr (VEB). Habitualmente, esta afecci\u00f3n compromete primariamente el tracto respiratorio superior (v\u00e9ase tambi\u00e9n Trastornos linfoproliferativos asociados al VEB). 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