{"id":13718,"date":"2020-11-20T23:47:01","date_gmt":"2020-11-20T23:47:01","guid":{"rendered":"https:\/\/dermatly.com\/mastocitoma\/"},"modified":"2026-03-10T16:48:37","modified_gmt":"2026-03-10T16:48:37","slug":"mastocitoma-2","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/it\/mastocitoma\/","title":{"rendered":"Mastocitoma"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Comprendiendo el Mastocitoma Cut\u00e1neo: Definici\u00f3n, Prevalencia y Caracter\u00edsticas<\/h1>\n<p>El mastocitoma representa una forma espec\u00edfica de mastocitosis cut\u00e1nea, caracterizada por la acumulaci\u00f3n localizada de <span class=\"term\" data-term-id=\"582\">mastocitos<\/span> formando una o varias <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> \u00fanicas en la piel [1].<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h2 class=\"colour--primary\">Mastocitoma<\/h2>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/masto__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Imagen de un mastocitoma cut\u00e1neo\">\n            <\/div>\n<p class=\"p-small\">Mastocitoma<\/p>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/mastob__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Mastocitoma mostrando el signo de Darier despu\u00e9s de frotar\">\n            <\/div>\n<p class=\"p-small\">La misma lesi\u00f3n despu\u00e9s de frotarla (Signo de Darier).<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>\u00bfA Qui\u00e9n Afecta Principalmente el Mastocitoma?<\/h2>\n<p>El diagn\u00f3stico del mastocitoma se realiza con mayor frecuencia en la poblaci\u00f3n infantil, espec\u00edficamente entre el nacimiento y los 3 meses de edad. Es un hallazgo infrecuente en adultos [2]. Es importante notar que el mastocitoma generalmente no presenta un patr\u00f3n <span class=\"term\" data-term-id=\"849\">hereditario<\/span> o familiar.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>Causas Subyacentes y Fisiopatolog\u00eda del Mastocitoma<\/h2>\n<p>La formaci\u00f3n del mastocitoma est\u00e1 intr\u00ednsecamente ligada a alteraciones gen\u00e9ticas. Espec\u00edficamente, una mutaci\u00f3n en el <a href=\"#\">EQUIPO <span class=\"term\" data-term-id=\"774\">KIT<\/span>, que codifica una tirosina transmembrana <span class=\"term\" data-term-id=\"782\">receptor<\/span> ubicado en la membrana del <span class=\"term\" data-term-id=\"633\">mastocito<\/span>, es responsable de la proliferaci\u00f3n y la funci\u00f3n anormal de estas c\u00e9lulas [3].<\/a><\/p>\n<p>Cuando estos mastocitos se activan, liberan mediadores inflamatorios potentes como la <span class=\"term\" data-term-id=\"856\">histamina<\/span> y otras sustancias qu\u00edmicas. Esta liberaci\u00f3n resulta en s\u00edntomas cut\u00e1neos caracter\u00edsticos, incluyendo enrojecimiento <span class=\"term\" data-term-id=\"324\">localizado<\/span>, edema, prurito (picaz\u00f3n) y, en ocasiones, la formaci\u00f3n de ves\u00edculas o ampollas.<\/p>\n<h2>Manifestaciones Cl\u00ednicas T\u00edpicas del Mastocitoma<\/h2>\n<p>Generalmente, los pacientes presentan entre una y tres lesiones de mastocitoma que aparecen durante los primeros meses de vida. Estas lesiones cut\u00e1neas pueden localizarse en cualquier \u00e1rea del cuerpo.<\/p>\n<p>Las caracter\u00edsticas cl\u00ednicas distintivas del mastocitoma incluyen:<\/p>\n<ul>\n<li>Una lesi\u00f3n bien definida, sea una <span class=\"term\" data-term-id=\"174\">m\u00e1cula<\/span>, p\u00e1pula, o una <span class=\"term\" data-term-id=\"235\">placa<\/span> <span class=\"term\" data-term-id=\"1741\">endurecida<\/span>, con un di\u00e1metro que usualmente oscila entre 1 y 5 cm.<\/li>\n<li>La superficie de la lesi\u00f3n puede presentar una textura irregular, a menudo descrita como apariencia de piel de naranja.<\/li>\n<li>La coloraci\u00f3n es variable: puede ser roja, rosada, amarillenta o marr\u00f3n.<\/li>\n<li>Suele cursar con picaz\u00f3n intermitente, la cual se intensifica notablemente al frotarla.<\/li>\n<li>El frotamiento provoca una reacci\u00f3n urticarial inmediata o r\u00e1pida (enrojecimiento e hinchaz\u00f3n) que persiste durante aproximadamente 15 minutos; este fen\u00f3meno constituye un resultado positivo para el <span class=\"term\" data-term-id=\"50\">signo de Darier<\/span>. En algunos casos, la fricci\u00f3n puede inducir la formaci\u00f3n de una ampolla.<\/li>\n<\/ul>\n<p>En raras ocasiones, si hay una liberaci\u00f3n significativa de histamina por parte de los mastocitos en la piel, puede manifestarse un enrojecimiento <span class=\"term\" data-term-id=\"308\">generalizado<\/span> o localizado.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h2 class=\"colour--primary\">Signo de Darier en Mastocitoma<\/h2>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <!-- Media element preserved verbatim -->\n            <\/div>\n<\/p><\/div>\n<\/section>\n<\/section>\n<figure>\n    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/mastocytoma-hand__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.JPG\" alt=\"Manifestaci\u00f3n visible de un mastocitoma en la mano de un paciente\"><br \/>\n<\/figure>\n<div class=\"imageLinkBlock__item__image\">\n    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/mastocytoma-hand-Darier-sign__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.JPG\" alt=\"Signo de Darier caracter\u00edstico en un mastocitoma\">\n<\/div>\n<p class=\"p-small\">Signo de Darier en mastocitoma<\/p>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h1>Abordaje Diagn\u00f3stico del Mastocitoma Cut\u00e1neo<\/h1>\n<p>El diagn\u00f3stico del mastocitoma es frecuentemente cl\u00ednico, especialmente cuando se observa una manifestaci\u00f3n positiva del signo de Darier. La <span>dermatoscopia<\/span> (t\u00e9rmino interno ID: 2028) ofrece hallazgos inespec\u00edficos [4], y no se aprecian los patrones t\u00edpicos observados en el <span>nevo<\/span> melanoc\u00edtico (t\u00e9rminos internos ID: 353, 785). Generalmente, no se requieren pruebas sangu\u00edneas complementarias para establecer el diagn\u00f3stico inicial.<\/p>\n<p>La confirmaci\u00f3n histopatol\u00f3gica se obtiene mediante una <span>biopsia<\/span> cut\u00e1nea (t\u00e9rmino interno ID: 24). El an\u00e1lisis revela un <span>infiltrado<\/span> (t\u00e9rmino interno ID: 541) <span>monomorfo<\/span> (t\u00e9rmino interno ID: 326) de c\u00e9lulas mononucleares que reaccionan positivamente tanto a las tinciones de c-KIT como a la inmunoperoxidasa para triptasa [2,3].<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n            <!-- \/340621630\/dermnet_mobile_after4sections_300x250' --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-9\" class=\"[ js-hideable ]\"><\/div>\n<p>            <script>\n                if (ads_screenwidth < 780 ) {\n                    var inline = document.createElement(\"div\");\n                    var ad = document.createElement(\"div\");\n\n                    ad.id = 'div-gpt-ad-1484122037505-9';\n                    ad.style.height=\"250px\";\n                    ad.style.width=\"300px;\";\n\n                    inline.appendChild(ad);\n                    inline.className = \"inline\";\n                    var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-9\");\n                    placeholder.parentNode.replaceChild(inline, placeholder);\n                    (function () {\n                        googletag.cmd.push(function () {\n                            googletag.display('div-gpt-ad-1484122037505-9');\n                        });\n                    })();\n                }\n            <\/script>\n        <\/div>\n<\/p><\/div>\n<\/div>\n<h2>Diagn\u00f3stico Diferencial Fundamental del Mastocitoma<\/h2>\n<p>Inicialmente, si el mastocitoma presenta sintomatolog\u00eda como picaz\u00f3n, es habitual su confusi\u00f3n con una reacci\u00f3n <span>persistente<\/span> (t\u00e9rmino interno ID: 2193) a la picadura de un insecto. Si la lesi\u00f3n carece de prurito, debe considerarse un <span>nevo<\/span> melanoc\u00edtico <span>cong\u00e9nito<\/span> (t\u00e9rmino interno ID: 1036) o de aparici\u00f3n temprana.<\/p>\n<p>Cuando se identifican cuatro o m\u00e1s lesiones de mastocitos, la descripci\u00f3n cl\u00ednica m\u00e1s adecuada corresponde a la mastocitosis cut\u00e1nea <span>maculopapular<\/span> (t\u00e9rmino interno ID: 938), tambi\u00e9n conocida como <span>urticaria<\/span> pigmentosa (t\u00e9rmino interno ID: 1646).<\/p>\n<p>Si el signo de Darier es positivo en un mastocitoma que aparece en la edad adulta, es imperativo descartar la posibilidad de una mastocitosis cut\u00e1nea m\u00e1s <span>extendida<\/span> (t\u00e9rmino interno ID: 309) o mastocitosis <span>sist\u00e9mica<\/span> (t\u00e9rmino interno ID: 380). Esta sospecha se intensifica si el paciente experimenta s\u00edntomas sist\u00e9micos, como episodios de ruborizaci\u00f3n.<\/p>\n<h2>Opciones de Tratamiento para el Mastocitoma<\/h2>\n<p>Es fundamental evitar el rascado o cualquier tipo de <span>trauma<\/span> (t\u00e9rmino interno ID: 1365) sobre la lesi\u00f3n. Esta prevenci\u00f3n ayuda a minimizar la aparici\u00f3n de prurito, edema y formaci\u00f3n de ves\u00edculas.<\/p>\n<p>Cuando la picaz\u00f3n causada por el mastocitoma es intensa, el alivio frecuentemente se logra mediante la administraci\u00f3n de antihistam\u00ednicos orales. Adicionalmente, se ha documentado la eficacia del <span>ung\u00fcento<\/span> (t\u00e9rmino interno ID: 1122) de tacrolimus<br \/>\n<span class=\"term\" data-term-id=\"1330\">t\u00f3pico<\/span> para mitigar los s\u00edntomas asociados a estos n\u00f3dulos.<\/p>\n<p>La extirpaci\u00f3n quir\u00fargica de un mastocitoma es una opci\u00f3n viable, especialmente si se localiza en zonas est\u00e9ticamente sensibles [3]. Sin embargo, es importante considerar que la reacci\u00f3n de <span>urticaci\u00f3n<\/span> localizada puede <span>persistir<\/span> (t\u00e9rmino interno ID: 2191) dentro de la <span>cicatriz<\/span> (t\u00e9rmino interno ID: 1191) resultante de la intervenci\u00f3n [2].<\/p>\n<h2>Pron\u00f3stico y Evoluci\u00f3n del Mastocitoma<\/h2>\n<p>Los mastocitomas que se desarrollan durante la infancia suelen presentar una regresi\u00f3n espont\u00e1nea, desapareciendo generalmente antes de que el individuo alcance la pubertad [1].<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Comprendiendo el Mastocitoma Cut\u00e1neo: Definici\u00f3n, Prevalencia y Caracter\u00edsticas El mastocitoma representa una forma espec\u00edfica de mastocitosis cut\u00e1nea, caracterizada por la acumulaci\u00f3n localizada de mastocitos formando una o varias lesiones \u00fanicas en la piel [1]. Mastocitoma Mastocitoma La misma lesi\u00f3n despu\u00e9s de frotarla (Signo de Darier). \u00bfA Qui\u00e9n Afecta Principalmente el Mastocitoma? El diagn\u00f3stico del mastocitoma [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":13721,"parent":0,"template":"","glossary-cat":[],"class_list":["post-13718","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Mastocitoma - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/it\/mastocitoma-2\/\" \/>\n<meta property=\"og:locale\" content=\"it_IT\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Mastocitoma\" \/>\n<meta property=\"og:description\" content=\"Comprendiendo el Mastocitoma Cut\u00e1neo: Definici\u00f3n, Prevalencia y Caracter\u00edsticas El mastocitoma representa una forma espec\u00edfica de mastocitosis cut\u00e1nea, caracterizada por la acumulaci\u00f3n localizada de mastocitos formando una o varias lesiones \u00fanicas en la piel [1]. Mastocitoma Mastocitoma La misma lesi\u00f3n despu\u00e9s de frotarla (Signo de Darier). \u00bfA Qui\u00e9n Afecta Principalmente el Mastocitoma? 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Mastocitoma Mastocitoma La misma lesi\u00f3n despu\u00e9s de frotarla (Signo de Darier). \u00bfA Qui\u00e9n Afecta Principalmente el Mastocitoma? 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