{"id":8903,"date":"2020-11-15T16:24:57","date_gmt":"2020-11-15T16:24:57","guid":{"rendered":"https:\/\/dermatly.com\/patologia-del-eritema-elevatum-diutinum\/"},"modified":"2026-03-10T16:04:08","modified_gmt":"2026-03-10T16:04:08","slug":"erythema-elevatum-diutinum-pathology","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/en\/patologia-del-eritema-elevatum-diutinum\/","title":{"rendered":"Pathology of Erythema Elevatum Diutinum"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Eritema Elevatum Diutinum: Caracter\u00edsticas y Hallazgos Histopatol\u00f3gicos<\/h1>\n<p>El <strong>eritema elevatum diutinum<\/strong> (EED) es una afecci\u00f3n dermatol\u00f3gica <span class=\"term\" data-term-id=\"319\">cr\u00f3nica<\/span> y poco frecuente. Se manifiesta t\u00edpicamente a trav\u00e9s de la aparici\u00f3n de <span class=\"term\" data-term-id=\"366\">p\u00e1pulas<\/span> y <span class=\"term\" data-term-id=\"367\">n\u00f3dulos<\/span> de color rojo-marr\u00f3n. Estas lesiones suelen localizarse en las superficies de extensi\u00f3n muscular, especialmente en el <span class=\"term\" data-term-id=\"71\">dorsal<\/span> de las manos. Adem\u00e1s de las manifestaciones cut\u00e1neas, es com\u00fan que los pacientes presenten s\u00edntomas <span class=\"term\" data-term-id=\"380\">sist\u00e9micos<\/span>, como <span class=\"term\" data-term-id=\"601\">artralgia<\/span>. Se ha documentado su asociaci\u00f3n con diversas condiciones <span class=\"term\" data-term-id=\"1522\">hematol\u00f3gicas<\/span> y <span class=\"term\" data-term-id=\"2347\">reumatol\u00f3gicas<\/span>, lo cual subraya la necesidad de una evaluaci\u00f3n integral.<\/p>\n<h2>Histopatolog\u00eda Detallada del Eritema Elevatum Diutinum<\/h2>\n<p>La <span class=\"term\" data-term-id=\"128\">histolog\u00eda<\/span> del eritema elevatum diutinum revela hallazgos caracter\u00edsticos en la dermis. Es importante notar la persistencia (preservaci\u00f3n) de la dermis papilar y la regi\u00f3n <span class=\"term\" data-term-id=\"1625\">perianexial<\/span> (visualizada en Figuras 1 y 2). Microsc\u00f3picamente, se observa un <span class=\"term\" data-term-id=\"543\">infiltrado<\/span> <span class=\"term\" data-term-id=\"753\">vascular<\/span> que afecta la dermis superior y media. Este infiltrado est\u00e1 compuesto predominantemente por <span class=\"term\" data-term-id=\"442\">neutr\u00f3filos<\/span>, aunque tambi\u00e9n se identifican <span class=\"term\" data-term-id=\"421\">linfocitos<\/span>, <span class=\"term\" data-term-id=\"448\">eosin\u00f3filos<\/span> y <span class=\"term\" data-term-id=\"1513\">c\u00e9lulas plasm\u00e1ticas<\/span> en menor proporci\u00f3n (Figuras 3, 4, 5).<\/p>\n<p>En las lesiones m\u00e1s recientes, es frecuente identificar leucocitoclasia (Figura 5). A medida que las lesiones evolucionan, se produce <span class=\"term\" data-term-id=\"260\">esclerosis<\/span> d\u00e9rmica, acompa\u00f1ada de la presencia persistente de <span class=\"term\" data-term-id=\"2209\">c\u00e9lulas plasm\u00e1ticas<\/span> y focos residuales de <span class=\"term\" data-term-id=\"1388\">vasculitis<\/span> leucocitocl\u00e1stica. En algunos casos, este proceso de esclerosis puede ser marcado y manifestarse con un patr\u00f3n estoriforme (Figura 1 y 4), lo que representa una caracter\u00edstica morfol\u00f3gica distintiva de esta <span class=\"term\" data-term-id=\"60\">dermatosis<\/span>.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h2 class=\"colour--primary\">Im\u00e1genes Correlacionando la Patolog\u00eda del Eritema Elevatum Diutinum<\/h2>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<figure>\n                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/eedfigure1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microfotograf\u00eda de histopatolog\u00eda de Eritema Elevatum Diutinum, mostrando esclerosis con un patr\u00f3n estoriforme.\"><figcaption>Figura 1<\/figcaption><\/figure>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n<figure>\n                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/eedfigure2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Histopatolog\u00eda de EED que demuestra preservaci\u00f3n de la dermis papilar.\"><figcaption>Figura 2<\/figcaption><\/figure>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n<figure>\n                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/eedfigure3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Histopatolog\u00eda mostrando infiltrado vascular con predominio de neutr\u00f3filos.\"><figcaption>Figura 3<\/figcaption><\/figure>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n<figure>\n                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/eedfigure4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Imagen histol\u00f3gica correlacionada con la esclerosis estoriforme observada en EED.\"><figcaption>Figura 4<\/figcaption><\/figure>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n<figure>\n                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/eedfigure5__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Detalle histopatol\u00f3gico que ilustra la leucocitoclasia com\u00fan en lesiones recientes de EED.\"><figcaption>Figura 5<\/figcaption><\/figure>\n<\/p><\/div>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n    <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 -->\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<p>Entender la presentaci\u00f3n cl\u00ednica del eritema elevatum diutinum, junto con sus hallazgos distintivos en la biopsia de piel, es crucial para el diagn\u00f3stico preciso de esta rara vasculitis. La correlaci\u00f3n entre los signos cut\u00e1neos y las posibles comorbilidades sist\u00e9micas siempre debe ser considerada en el manejo del paciente.<\/p>\n<\/section>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p><script>\n    if (ads_screenwidth < 780 ) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-8';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-8');\n            });\n        })();\n    }\n<\/script><\/p>\n<h1>Diagn\u00f3stico Diferencial Detallado del Eritema Elevatum Diutinum<\/h1>\n<p>Para establecer un diagn\u00f3stico preciso del Eritema Elevatum Diutinum (EED), es crucial distinguirlo de otras afecciones cut\u00e1neas con presentaciones cl\u00ednicas similares. A continuaci\u00f3n, se detallan las condiciones clave para el diagn\u00f3stico diferencial:<\/p>\n<h2>Condiciones a Diferenciar del Eritema Elevatum Diutinum<\/h2>\n<p><span class=\"term\" data-term-id=\"113\">Granuloma Faciale<\/span>: Algunos expertos consideran que esta condici\u00f3n podr\u00eda ser una manifestaci\u00f3n del mismo trastorno, pero limitada a la regi\u00f3n facial. Ambos procesos cl\u00ednicos comparten caracter\u00edsticas de vasculitis esclerosante de vasos peque\u00f1os. Es importante destacar que el granuloma facial generalmente presenta una menor asociaci\u00f3n con enfermedad sist\u00e9mica en comparaci\u00f3n con el EED.<\/p>\n<p>Vasculitis Leucocitocl\u00e1stica: Las formas m\u00e1s agudas de vasculitis leucocitocl\u00e1stica exhiben un <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> celular menos denso. Cl\u00ednicamente, estas formas tienden a mostrar una mayor <span class=\"term\" data-term-id=\"692\">eritrocito<\/span> <span class=\"term\" data-term-id=\"607\">extravasaci\u00f3n<\/span> en comparaci\u00f3n con el EED establecido.<\/p>\n<p>Dermatosis Neutrof\u00edlicas Agudas: Aunque existen distinciones cl\u00ednicas claras, las etapas iniciales de las lesiones del EED pueden asemejarse al S\u00edndrome de Sweet y otras <span class=\"term\" data-term-id=\"329\">dermatosis<\/span> caracterizadas por predominio neutrof\u00edlico.<\/p>\n<p>Dermatofibroma: Las fases m\u00e1s tard\u00edas y <span class=\"term\" data-term-id=\"369\">fibr\u00f3tico<\/span> del Eritema Elevatum Diutinum pueden simular un dermatofibroma. Sin embargo, las lesiones de EED carecen del patr\u00f3n caracter\u00edstico de atrapamiento de <span class=\"term\" data-term-id=\"39\">col\u00e1geno<\/span> perif\u00e9rico y de la <span class=\"term\" data-term-id=\"136\">hiperplasia<\/span> <span class=\"term\" data-term-id=\"846\">epid\u00e9rmica<\/span> que se observa t\u00edpicamente en el dermatofibroma.<\/p>\n<p><span class=\"term\" data-term-id=\"102\">Fibrosis<\/span> Angioc\u00e9ntrica Eosinof\u00edlica: Esta condici\u00f3n se distingue por la presencia de fibrosis (que ocasionalmente puede adoptar un patr\u00f3n estoriforme) que envuelve peque\u00f1as <span class=\"term\" data-term-id=\"1962\">arterias<\/span>, com\u00fanmente localizadas en la \u00f3rbita y el tracto respiratorio superior. Se acompa\u00f1a de <span class=\"term\" data-term-id=\"490\">infiltrados<\/span> <span class=\"term\" data-term-id=\"542\">inflamatorios<\/span> mixtos con una marcada predominancia de eosin\u00f3filos. Recientemente, se ha documentado una posible asociaci\u00f3n entre esta entidad y niveles elevados de IgG4.<\/p>\n<p>Para un diagn\u00f3stico definitivo, la correlaci\u00f3n entre la presentaci\u00f3n cl\u00ednica y los hallazgos histopatol\u00f3gicos es fundamental para diferenciar el Eritema Elevatum Diutinum de estas patolog\u00edas similares, asegurando el tratamiento m\u00e1s adecuado para el paciente.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Eritema Elevatum Diutinum: Caracter\u00edsticas y Hallazgos Histopatol\u00f3gicos El eritema elevatum diutinum (EED) es una afecci\u00f3n dermatol\u00f3gica cr\u00f3nica y poco frecuente. Se manifiesta t\u00edpicamente a trav\u00e9s de la aparici\u00f3n de p\u00e1pulas y n\u00f3dulos de color rojo-marr\u00f3n. Estas lesiones suelen localizarse en las superficies de extensi\u00f3n muscular, especialmente en el dorsal de las manos. Adem\u00e1s de las [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":8909,"parent":0,"template":"","glossary-cat":[],"class_list":["post-8903","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda del eritema elevatum diutinum - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/en\/erythema-elevatum-diutinum-pathology\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda del eritema elevatum diutinum\" \/>\n<meta property=\"og:description\" content=\"Eritema Elevatum Diutinum: Caracter\u00edsticas y Hallazgos Histopatol\u00f3gicos El eritema elevatum diutinum (EED) es una afecci\u00f3n dermatol\u00f3gica cr\u00f3nica y poco frecuente. 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Se manifiesta t\u00edpicamente a trav\u00e9s de la aparici\u00f3n de p\u00e1pulas y n\u00f3dulos de color rojo-marr\u00f3n. Estas lesiones suelen localizarse en las superficies de extensi\u00f3n muscular, especialmente en el dorsal de las manos. 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