{"id":5293,"date":"2020-11-12T09:56:26","date_gmt":"2020-11-12T09:56:26","guid":{"rendered":"https:\/\/dermatly.com\/patologia-del-penfigoide-cicatricial-de-brunsting-perry\/"},"modified":"2026-03-10T16:06:03","modified_gmt":"2026-03-10T16:06:03","slug":"brunsting-perry-cicatricial-pemphigoid-pathology","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/en\/patologia-del-penfigoide-cicatricial-de-brunsting-perry\/","title":{"rendered":"Pathology of Brunsting-Perry Cicatricial Pemphigoid"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Entendiendo el Penfigoide Cicatricial de Brunsting-Perry: Hallazgos Cl\u00ednicos y Patol\u00f3gicos<\/h1>\n<p>El <span class=\"term\" data-term-id=\"36\">penfigoide cicatricial<\/span> de Brunsting-Perry se define como una presentaci\u00f3n infrecuente del penfigoide cicatricial <span class=\"term\" data-term-id=\"324\">localizado<\/span>, afectando predominantemente las \u00e1reas de la cabeza y el cuello. Lo que distingue a esta variante es su marcada tendencia a <strong style=\"font-weight: normal;\">no involucrar las membranas de la <span class=\"term\" data-term-id=\"1018\">mucosa<\/span><\/strong>, a diferencia de la forma cl\u00e1sica del penfigoide cicatricial. En el proceso diagn\u00f3stico diferencial, es fundamental distinguirlo del penfigoide <span class=\"term\" data-term-id=\"498\">bulloso<\/span>, dado que la cicatrizaci\u00f3n en la variante de Brunsting-Perry es mucho m\u00e1s prominente.<\/p>\n<h2>Evaluaci\u00f3n Histol\u00f3gica y Caracter\u00edsticas Dermatopatol\u00f3gicas<\/h2>\n<p>El estudio <span class=\"term\" data-term-id=\"867\">microsc\u00f3pico<\/span> de las lesiones asociadas al penfigoide cicatricial de Brunsting-Perry t\u00edpicamente revela la formaci\u00f3n de ampollas <span class=\"term\" data-term-id=\"2429\">subepid\u00e9rmicas<\/span>. Estas ampollas se encuentran acompa\u00f1adas por un <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> de <span class=\"term\" data-term-id=\"541\">c\u00e9lulas<\/span> <span class=\"term\" data-term-id=\"490\">inflamatorias<\/span> cuya composici\u00f3n puede ser variable. Inicialmente, las <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> puede presentar peque\u00f1os <span class=\"term\" data-term-id=\"1454\">microabscesos<\/span> localizados en la regi\u00f3n papilar d\u00e9rmica.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Visualizaci\u00f3n Patol\u00f3gica del Penfigoide Cicatricial de Brunsting-Perry<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 1\">\n                <\/div>\n<p class=\"p-small\">Figura 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 2\">\n                <\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 3\">\n                <\/div>\n<p class=\"p-small\">Figura 3<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 4\">\n                <\/div>\n<p class=\"p-small\">Figura 4<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-5__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 5\">\n                <\/div>\n<p class=\"p-small\">Figura 5<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/brunsting-perry-fig-6__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Im\u00e1genes histopatol\u00f3gicas que muestran las caracter\u00edsticas del penfigoide cicatricial de Brunsting-Perry, Figura 6\">\n                <\/div>\n<p class=\"p-small\">Figura 6<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<p>Im\u00e1genes cortes\u00eda del Dr. Duncan Lamont, Hospital Waikato<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\"><\/div>\n<\/section>\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n        <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>        <script>\n            if (ads_screenwidth\n<\/script><br \/>\n        <script>\n            if (window.innerWidth < 780) {\n                var inline = document.createElement(\"div\");\n                var ad = document.createElement(\"div\");\n\n                ad.id = 'div-gpt-ad-1484122037505-8';\n                ad.style.height = \"250px\";\n                ad.style.width = \"300px;\";\n\n                inline.appendChild(ad);\n                inline.className = \"inline\";\n                var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                placeholder.parentNode.replaceChild(inline, placeholder);\n                (function () {\n                    googletag.cmd.push(function () {\n                        googletag.display('div-gpt-ad-1484122037505-8');\n                    });\n                })();\n            }\n        <\/script>\n    <\/div>\n<\/div>\n<section>\n<h1>Evaluaci\u00f3n Diagn\u00f3stica del Penfigoide Cicatricial de Brunsting-Perry<\/h1>\n<p>La <strong>Inmunofluorescencia<\/strong> constituye el pilar inicial del an\u00e1lisis, revelando dep\u00f3sitos de IgG y\/o C3 localizados precisamente en la uni\u00f3n de la <span class=\"term\" data-term-id=\"21\"><span class=\"term\" data-term-id=\"1970\">membrana basal<\/span><\/span> d\u00e9rmica.<\/p>\n<p>En cuanto a la evaluaci\u00f3n ultraestructural mediante <strong>Microscop\u00eda de electrones<\/strong>, se observa una separaci\u00f3n caracter\u00edstica en la regi\u00f3n de la subl\u00e1mina densa. Es importante destacar que la <span class=\"term\" data-term-id=\"831\">l\u00e1mina<\/span> <span class=\"term\" data-term-id=\"2356\">basal<\/span> permanece \u00edntegra, mientras que las <span class=\"term\" data-term-id=\"1709\">fibrillas<\/span> de anclaje quedan visibles y expuestas en el borde superior de la ampolla resultante.<\/p>\n<h2>Distinci\u00f3n Cl\u00ednica: Diagn\u00f3stico Diferencial del Penfigoide Cicatricial de Brunsting-Perry<\/h2>\n<p>Establecer el <strong>diagn\u00f3stico diferencial<\/strong> preciso es crucial para diferenciar esta entidad de otras patolog\u00edas de formaci\u00f3n de ampollas. El principal aspecto a considerar en la diferenciaci\u00f3n incluye:<\/p>\n<ul>\n<li>Penfigoide ampolloso localizado<\/li>\n<\/ul>\n<p>Una correcta identificaci\u00f3n de estas diferencias cl\u00ednicas y patol\u00f3gicas asegura la implementaci\u00f3n del tratamiento m\u00e1s adecuado para el paciente con Penfigoide Cicatricial de Brunsting-Perry.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Entendiendo el Penfigoide Cicatricial de Brunsting-Perry: Hallazgos Cl\u00ednicos y Patol\u00f3gicos El penfigoide cicatricial de Brunsting-Perry se define como una presentaci\u00f3n infrecuente del penfigoide cicatricial localizado, afectando predominantemente las \u00e1reas de la cabeza y el cuello. Lo que distingue a esta variante es su marcada tendencia a no involucrar las membranas de la mucosa, a diferencia [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":5300,"parent":0,"template":"","glossary-cat":[],"class_list":["post-5293","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda del penfigoide cicatricial de Brunsting-Perry - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/en\/brunsting-perry-cicatricial-pemphigoid-pathology\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda del penfigoide cicatricial de Brunsting-Perry\" \/>\n<meta property=\"og:description\" content=\"Entendiendo el Penfigoide Cicatricial de Brunsting-Perry: Hallazgos Cl\u00ednicos y Patol\u00f3gicos El penfigoide cicatricial de Brunsting-Perry se define como una presentaci\u00f3n infrecuente del penfigoide cicatricial localizado, afectando predominantemente las \u00e1reas de la cabeza y el cuello. 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