{"id":2969,"date":"2020-11-08T17:59:35","date_gmt":"2020-11-08T17:59:35","guid":{"rendered":"https:\/\/dermatly.com\/patologia-del-angiomiofibroblastoma\/"},"modified":"2026-03-10T14:40:10","modified_gmt":"2026-03-10T14:40:10","slug":"angiomyofibroblastoma-pathology","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/en\/patologia-del-angiomiofibroblastoma\/","title":{"rendered":"Pathology of Angiomyofibroblastoma"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Angiofibromas: Caracter\u00edsticas Cl\u00ednicas e Histopatol\u00f3gicas<\/h1>\n<p>El angiomiofibroblastoma (AMF) se clasifica como un <span class=\"term\" data-term-id=\"22\">tumor benigno<\/span> de los tejidos blandos que afecta espec\u00edficamente los genitales externos.<\/p>\n<h2>Histolog\u00eda del Angiomiofibroblastoma<\/h2>\n<p>El examen <span class=\"term\" data-term-id=\"868\">microsc\u00f3pico<\/span> del angiomiofibroblastoma revela un tumor bien <span class=\"term\" data-term-id=\"37\">circunscrito<\/span>, aunque carece de una c\u00e1psula verdadera y presenta celularidad variable. Las regiones con baja celularidad muestran un predominio de material <span class=\"term\" data-term-id=\"1185\">col\u00e1geno<\/span> (Figura 1) o una matriz <span class=\"term\" data-term-id=\"191\">mixoide<\/span>, asociadas a vasos de tama\u00f1o peque\u00f1o a mediano. Por otro lado, las \u00e1reas hipercelulares, que suelen rodear a los vasos, se caracterizan por la presencia de c\u00e9lulas redondeadas a ovales con <span class=\"term\" data-term-id=\"729\">n\u00facleos<\/span> de morfolog\u00eda uniforme y escasa <span class=\"term\" data-term-id=\"1305\">atipia<\/span> (Figura 2). Ocasionalmente, es posible identificar c\u00e9lulas binucleadas o <span class=\"term\" data-term-id=\"736\">multinucleadas<\/span>.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Patolog\u00eda Detallada del Angiomiofibroblastoma<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/angiomyofibroblastoma-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Micrograf\u00eda que muestra la estructura colagenosa o mixoide t\u00edpica del angiomiofibroblastoma (Figura 1).\">\n            <\/div>\n<p class=\"p-small\">Figura 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/angiomyofibroblastoma-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Micrograf\u00eda que ilustra las c\u00e9lulas redondeadas\/ovales con n\u00facleos uniformes caracter\u00edsticas en \u00e1reas hipercelulares del angiomiofibroblastoma (Figura 2).\">\n            <\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>Estudios Especiales en el Diagn\u00f3stico del Angiomiofibroblastoma<\/h2>\n<p>Mediante la t\u00e9cnica de <span class=\"term\" data-term-id=\"1421\">inmunohistoqu\u00edmica<\/span>, las c\u00e9lulas tumorales del angiomiofibroblastoma t\u00edpicamente muestran positividad para la actina. Adicionalmente, es com\u00fan observar positividad para los marcadores hormonales, espec\u00edficamente <span class=\"term\" data-term-id=\"1844\">estr\u00f3geno<\/span> y <span class=\"term\" data-term-id=\"1841\">progesterona<\/span>.<\/p>\n<h2>Diagn\u00f3stico Diferencial en la Patolog\u00eda del Angiomiofibroblastoma<\/h2>\n<p>Es crucial diferenciar el AMF de otras entidades patol\u00f3gicas, especialmente el <span class=\"term\" data-term-id=\"1952\">angiomixoma agresivo<\/span>. Los angiomixomas agresivos tienden a ser tumores <span class=\"term\" data-term-id=\"611\">infiltrantes<\/span> y suelen alcanzar tama\u00f1os considerablemente mayores, a menudo superando los 5 cm. La existencia de tumores con caracter\u00edsticas morfol\u00f3gicas mixtas entre angiomiofibroblastoma y angiomixoma agresivo sugiere una posible relaci\u00f3n etiol\u00f3gica entre ambas entidades, lo cual requiere una correlaci\u00f3n patol\u00f3gica meticulosa.<\/p>\n<p>En resumen, el angiomiofibroblastoma es un tumor benigno de apariencia bien definida que requiere un an\u00e1lisis histopatol\u00f3gico detallado y el apoyo de estudios inmunohistoqu\u00edmicos para confirmar su diagn\u00f3stico y distinguirlo de lesiones infiltrantes como el angiomixoma agresivo.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Angiofibromas: Caracter\u00edsticas Cl\u00ednicas e Histopatol\u00f3gicas El angiomiofibroblastoma (AMF) se clasifica como un tumor benigno de los tejidos blandos que afecta espec\u00edficamente los genitales externos. Histolog\u00eda del Angiomiofibroblastoma El examen microsc\u00f3pico del angiomiofibroblastoma revela un tumor bien circunscrito, aunque carece de una c\u00e1psula verdadera y presenta celularidad variable. Las regiones con baja celularidad muestran un predominio [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":2972,"parent":0,"template":"","glossary-cat":[],"class_list":["post-2969","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda del angiomiofibroblastoma - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/en\/angiomyofibroblastoma-pathology\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda del angiomiofibroblastoma\" \/>\n<meta property=\"og:description\" content=\"Angiofibromas: Caracter\u00edsticas Cl\u00ednicas e Histopatol\u00f3gicas El angiomiofibroblastoma (AMF) se clasifica como un tumor benigno de los tejidos blandos que afecta espec\u00edficamente los genitales externos. Histolog\u00eda del Angiomiofibroblastoma El examen microsc\u00f3pico del angiomiofibroblastoma revela un tumor bien circunscrito, aunque carece de una c\u00e1psula verdadera y presenta celularidad variable. 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