{"id":17776,"date":"2020-11-24T04:38:00","date_gmt":"2020-11-24T04:38:00","guid":{"rendered":"https:\/\/dermatly.com\/patologia-superficial-del-fibromixoma-acral\/"},"modified":"2026-03-10T16:56:05","modified_gmt":"2026-03-10T16:56:05","slug":"superficial-acral-fibromyxoma-pathology","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/en\/patologia-superficial-del-fibromixoma-acral\/","title":{"rendered":"Superficial Pathology of Acral Fibromyxoma"},"content":{"rendered":"<section class=\"textBlock\">\n<p>El <a href=\"\/es\/terminologia\/496-acral-fibromixoma\" title=\"Fibromixoma acral\">fibromixoma acral superficial<\/a> se cataloga como una de las <a href=\"\/es\/terminologia\/2115-lesiones\" title=\"Lesiones\">lesiones<\/a> <a href=\"\/es\/terminologia\/22-benigno\" title=\"Benigno\">benignas<\/a> con predominio de un componente fibromixoide. Estas formaciones suelen ser peque\u00f1as, se manifiestan de forma aislada y exhiben una marcada <a href=\"\/es\/terminologia\/1227-predileccion\" title=\"Predilecci\u00f3n\">predilecci\u00f3n<\/a> por las extremidades distales, afectando en particular los dedos de manos y pies, e involucrando frecuentemente la regi\u00f3n de las <a href=\"\/es\/terminologia\/193-unas\" title=\"U\u00f1as\">u\u00f1as<\/a>.<\/p>\n<h2>An\u00e1lisis Histol\u00f3gico del Fibromixoma Acral Superficial<\/h2>\n<p>Desde una perspectiva microsc\u00f3pica, el fibromixoma acral superficial se caracteriza por ser una <a href=\"\/es\/terminologia\/164-lesion\" title=\"Lesi\u00f3n\">lesi\u00f3n<\/a> paucicelular de naturaleza fibromixoide, origin\u00e1ndose primariamente en la <a href=\"\/es\/terminologia\/61-dermis\" title=\"Dermis\">dermis<\/a> de las \u00e1reas acrales (Figura 1), con afectaci\u00f3n <a href=\"\/es\/terminologia\/900-subcutaneo\" title=\"Subcut\u00e1neo\">subcut\u00e1nea<\/a> frecuente. Las c\u00e9lulas observables poseen una morfolog\u00eda fusiforme o estrellada, inmersas en un <a href=\"\/es\/terminologia\/1655-estroma\" title=\"Estroma\">estroma<\/a> predominantemente fibromixoide (Figuras 2 y 3).<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Manifestaciones Patol\u00f3gicas Superficiales del Fibromixoma Acral<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/superficial-acral-fibromyxoma-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDE0XQ.jpg\" alt=\"Micrograf\u00eda que muestra la histolog\u00eda del fibromixoma acral superficial, Figura 1, destacando la estructura general de la lesi\u00f3n d\u00e9rmica.\">\n            <\/div>\n<p class=\"p-small\">Figura 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/superficial-acral-fibromyxoma-fig-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Micrograf\u00eda que ilustra la composici\u00f3n celular y estromal del fibromixoma acral superficial, Figura 2, con detalle de las c\u00e9lulas fusiformes.\">\n            <\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/superficial-acral-fibromyxoma-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Detalle del estroma mixoide en el fibromixoma acral superficial, Figura 3, mostrando la matriz extracelular caracter\u00edstica.\">\n            <\/div>\n<p class=\"p-small\">Figura 3<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>Exploraciones Complementarias Esenciales para el Fibromixoma Acral Superficial<\/h2>\n<p>Los perfiles inmunohistoqu\u00edmicos del fibromixoma acral superficial suelen ser positivos para los marcadores CD34 y EMA. Sumado a esto, es crucial observar la negatividad caracter\u00edstica de marcadores como S100, <a href=\"\/es\/terminologia\/1613-citoqueratinas\" title=\"Citoqueratinas\">citoqueratinas<\/a> y los anticuerpos dirigidos contra el m\u00fasculo liso.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>Estableciendo el Diagn\u00f3stico Diferencial con el Fibromixoma Acral Superficial<\/h2>\n<p><a href=\"\/es\/terminologia\/875-neurofibroma\" title=\"Neurofibroma\">Neurofibroma<\/a>: Esta condici\u00f3n tambi\u00e9n presenta un estroma con cualidades fibromixoides notables. La distinci\u00f3n fundamental reside en que el marcador S100 resultar\u00e1 positivo en el caso del neurofibroma.<\/p>\n<p>Perineurioma: En su variante histol\u00f3gica esclerosante, el perineurioma afecta con frecuencia las regiones acrales. No obstante, la alteraci\u00f3n <a href=\"\/es\/terminologia\/191-mixoides\" title=\"Mixoides\">mixoides<\/a> se observa con menor regularidad en estas lesiones. Ambas entidades (Perineurioma y Fibromixoma Acral Superficial) ser\u00e1n reactivas para EMA y negativas para S100. La evidencia de positividad para Glut-1, concurrente con la ausencia de reactividad para CD34, orientar\u00e1 el diagn\u00f3stico definitivo hacia el perineurioma.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>El fibromixoma acral superficial se cataloga como una de las lesiones benignas con predominio de un componente fibromixoide. Estas formaciones suelen ser peque\u00f1as, se manifiestan de forma aislada y exhiben una marcada predilecci\u00f3n por las extremidades distales, afectando en particular los dedos de manos y pies, e involucrando frecuentemente la regi\u00f3n de las u\u00f1as. An\u00e1lisis [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":17780,"parent":0,"template":"","glossary-cat":[],"class_list":["post-17776","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda superficial del fibromixoma acral - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/en\/superficial-acral-fibromyxoma-pathology\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda superficial del fibromixoma acral\" \/>\n<meta property=\"og:description\" content=\"El fibromixoma acral superficial se cataloga como una de las lesiones benignas con predominio de un componente fibromixoide. Estas formaciones suelen ser peque\u00f1as, se manifiestan de forma aislada y exhiben una marcada predilecci\u00f3n por las extremidades distales, afectando en particular los dedos de manos y pies, e involucrando frecuentemente la regi\u00f3n de las u\u00f1as. 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