{"id":15909,"date":"2020-11-22T14:12:02","date_gmt":"2020-11-22T14:12:02","guid":{"rendered":"https:\/\/dermatly.com\/patologia-del-pilomatricoma\/"},"modified":"2026-03-10T16:46:50","modified_gmt":"2026-03-10T16:46:50","slug":"pilomatricoma-pathology","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/en\/patologia-del-pilomatricoma\/","title":{"rendered":"Pathology of Pilomatricoma"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Diagn\u00f3stico Histol\u00f3gico del Pilomatricoma<\/h1>\n<p>El pilomatricoma es una neoplasia cut\u00e1nea que se origina, seg\u00fan la evidencia actual, a partir de las c\u00e9lulas de la <span class=\"term\" data-term-id=\"122\">matriz del cabello<\/span>.<\/p>\n<h2>Caracter\u00edsticas Histol\u00f3gicas Clave del Pilomatricoma<\/h2>\n<p>A baja magnificaci\u00f3n, el patr\u00f3n <span class=\"term\" data-term-id=\"474\">histopatol\u00f3gico<\/span> caracter\u00edstico del pilomatricoma se evidencia como un tumor noduloqu\u00edstico bien <span class=\"term\" data-term-id=\"37\">circunscrito<\/span> (Figura 2). Aunque se localiza principalmente en la <span class=\"term\" data-term-id=\"61\">dermis<\/span> profunda, no es inusual que se extienda hacia el tejido <span class=\"term\" data-term-id=\"900\">subcut\u00e1neo<\/span>.<\/p>\n<p>Estructuralmente, este tumor est\u00e1 compuesto por una proliferaci\u00f3n de c\u00e9lulas <span class=\"term\" data-term-id=\"1654\">basaloides<\/span> que emulan las c\u00e9lulas de la matriz capilar. Estas c\u00e9lulas experimentan maduraci\u00f3n hacia estructuras <span class=\"term\" data-term-id=\"449\">eosinof\u00edlicas<\/span>, las cuales carecen de <span class=\"term\" data-term-id=\"729\">n\u00facleos<\/span> y son conocidas como c\u00e9lulas sombra (Figuras 3 y 4). Esta zona de c\u00e9lulas sombra refleja la <span class=\"term\" data-term-id=\"1307\">diferenciaci\u00f3n<\/span> hacia la corteza del fol\u00edculo piloso. Es frecuente observar focos de <span class=\"term\" data-term-id=\"1044\">calcificaci\u00f3n<\/span> dentro de estas regiones de c\u00e9lulas sombra (Figura 5). Adem\u00e1s, es com\u00fan encontrar un <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> <span class=\"term\" data-term-id=\"859\">histiocitario<\/span> que incluye c\u00e9lulas <span class=\"term\" data-term-id=\"736\">multinucleadas<\/span> en los puntos de ruptura tisular (Figura 6).<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Ilustraciones de la Patolog\u00eda del Pilomatricoma<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDEyXQ.jpg\" alt=\"Figura 1: Ilustraci\u00f3n de la patolog\u00eda del pilomatricoma mostrando la estructura tumoral general.\"><\/div>\n<p class=\"p-small\">Figura 1<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Figura 2: Patr\u00f3n noduloqu\u00edstico bien circunscrito del pilomatricoma.\"><\/div>\n<p class=\"p-small\">Figura 2<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Figura 3: Detalle de las c\u00e9lulas basaloides y las c\u00e9lulas sombra en el pilomatricoma.\"><\/div>\n<p class=\"p-small\">figura 3<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Figura 4: Visi\u00f3n ampliada de las c\u00e9lulas sombra anucleadas caracter\u00edsticas del tumor.\"><\/div>\n<p class=\"p-small\">Figura 4<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure5__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Figura 5: \u00c1rea de calcificaci\u00f3n presente en las regiones de c\u00e9lulas sombra.\"><\/div>\n<p class=\"p-small\">Figura 5<\/p>\n<div class=\"imageLinkBlock__item__image\">\n<p>                        <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/PilomatricomaFigure6__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Figura 6: Infiltrado histiocitario y c\u00e9lulas multinucleadas observadas en sitios inflamatorios.\"><\/div>\n<p class=\"p-small\">Figura 6<\/p>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>Uso de Tinciones Especiales en el Diagn\u00f3stico del Pilomatricoma<\/h2>\n<p>Generalmente, no se requiere la aplicaci\u00f3n de tinciones especiales para confirmar el diagn\u00f3stico histol\u00f3gico de pilomatricoma. No obstante, la tinci\u00f3n especial de Von Kossa puede ser \u00fatil para resaltar y confirmar la presencia de dep\u00f3sitos de calcio en la muestra tisular.<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                        <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 -->\n                    <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<p>Comprender la histolog\u00eda es fundamental para diferenciar el pilomatricoma de otros tumores cut\u00e1neos anexiales, garantizando un manejo cl\u00ednico adecuado.<\/p>\n<\/section>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p><script>\n    if (ads_screenwidth < 780 ) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-8';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-8');\n            });\n        })();\n    }\n<\/script>\n<\/div>\n<\/div>\n<section>\n<h2>Variantes Histol\u00f3gicas del Pilomatricoma: Caracter\u00edsticas Especiales<\/h2>\n<p>El pilomatricoma presenta variantes histol\u00f3gicas notables. Una de ellas es el <strong>pilomatricoma pigmentado<\/strong>, que se observa en hasta un 11% de los casos. Esta pigmentaci\u00f3n se debe a un incremento en el dep\u00f3sito de <strong>melanina<\/strong> o a una <strong>hiperplasia<\/strong> notoria de <strong>melanocitos<\/strong>.<\/p>\n<p>Dado que los melanocitos residen de forma natural dentro de la matriz capilar, su presencia en peque\u00f1as cantidades dentro de la proliferaci\u00f3n de c\u00e9lulas basaloideas es esperable. Sin embargo, cuando existe una hiperplasia <strong>melanoc\u00edtica<\/strong> marcada, se teoriza que podr\u00eda ser una respuesta secundaria a la exposici\u00f3n a est\u00edmulos <strong>UV<\/strong>.<\/p>\n<h2>Diagn\u00f3stico Diferencial Clave del Pilomatricoma<\/h2>\n<p>Es fundamental diferenciar el pilomatricoma de otras formaciones tumorales con constituyentes celulares similares. Uno de los principales focos de distinci\u00f3n es el <strong>Matricoma<\/strong>.<\/p>\n<p>El <strong>Matricoma<\/strong>, inicialmente documentado por Ackermann, comparte los mismos componentes celulares b\u00e1sicos que el pilomatricoma, pero se distingue por su configuraci\u00f3n. Mientras que el pilomatricoma t\u00edpicamente exhibe un componente qu\u00edstico pronunciado, el matricoma tiende a ser un tumor predominantemente basaloide, a menudo <strong>nodular<\/strong> o multinodular. Adem\u00e1s, el matricoma solo presenta \u00e1reas limitadas de formaci\u00f3n de c\u00e9lulas sombra, careciendo del patr\u00f3n qu\u00edstico caracter\u00edstico.<\/p>\n<p>Otra entidad a considerar es el <strong>Matricoma Melanoc\u00edtico<\/strong>. Este es un tumor poco frecuente y se considera probablemente una variante del matricoma, siguiendo la misma l\u00f3gica que el pilomatricoma pigmentado es una variante del pilomatricoma est\u00e1ndar. Sus contornos y componentes celulares parecen id\u00e9nticos a los del matricoma, pero se distingue por la adici\u00f3n de una proliferaci\u00f3n melanoc\u00edtica y, posiblemente, por la ausencia de calcificaci\u00f3n en las c\u00e9lulas sombra.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Diagn\u00f3stico Histol\u00f3gico del Pilomatricoma El pilomatricoma es una neoplasia cut\u00e1nea que se origina, seg\u00fan la evidencia actual, a partir de las c\u00e9lulas de la matriz del cabello. Caracter\u00edsticas Histol\u00f3gicas Clave del Pilomatricoma A baja magnificaci\u00f3n, el patr\u00f3n histopatol\u00f3gico caracter\u00edstico del pilomatricoma se evidencia como un tumor noduloqu\u00edstico bien circunscrito (Figura 2). Aunque se localiza principalmente [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":15916,"parent":0,"template":"","glossary-cat":[],"class_list":["post-15909","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda del pilomatricoma - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/en\/pilomatricoma-pathology\/\" \/>\n<meta property=\"og:locale\" content=\"en_US\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda del pilomatricoma\" \/>\n<meta property=\"og:description\" content=\"Diagn\u00f3stico Histol\u00f3gico del Pilomatricoma El pilomatricoma es una neoplasia cut\u00e1nea que se origina, seg\u00fan la evidencia actual, a partir de las c\u00e9lulas de la matriz del cabello. Caracter\u00edsticas Histol\u00f3gicas Clave del Pilomatricoma A baja magnificaci\u00f3n, el patr\u00f3n histopatol\u00f3gico caracter\u00edstico del pilomatricoma se evidencia como un tumor noduloqu\u00edstico bien circunscrito (Figura 2). 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