{"id":13432,"date":"2020-11-20T14:30:23","date_gmt":"2020-11-20T14:30:23","guid":{"rendered":"https:\/\/dermatly.com\/arteritis-linfocitica-trombofilica\/"},"modified":"2026-03-10T16:33:34","modified_gmt":"2026-03-10T16:33:34","slug":"lymphozytisch-thrombophile-arteriitis","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/de\/arteritis-linfocitica-trombofilica\/","title":{"rendered":"Arteritis linfoc\u00edtica trombof\u00edlica"},"content":{"rendered":"<p>\u00ab`html<\/p>\n<section class=\"textBlock\">\n<h1>Arteritis Linfoc\u00edtica Trombof\u00edlica: Definici\u00f3n, Causas y Presentaci\u00f3n Cl\u00ednica<\/h1>\n<h2 id=\"que-es-arteritis-linfocitica-trombofilica\">Definici\u00f3n de Arteritis Linfoc\u00edtica Trombof\u00edlica<\/h2>\n<p>La arteritis linfoc\u00edtica trombof\u00edlica se clasifica como una <span class=\"term\" data-term-id=\"949\">primaria<\/span> <span class=\"term\" data-term-id=\"1091\">vasculitis<\/span> linfoc\u00edtica. Cl\u00ednicamente, se manifiesta a trav\u00e9s de <span class=\"term\" data-term-id=\"1349\">livedo<\/span> racemosa o <span class=\"term\" data-term-id=\"1063\">macular<\/span> <span class=\"term\" data-term-id=\"135\">hiperpigmentaci\u00f3n<\/span>. Histol\u00f3gicamente, presenta hallazgos distintivos que afectan a las <span class=\"term\" data-term-id=\"1962\">arterias<\/span> peque\u00f1as y medianas localizadas en la <span class=\"term\" data-term-id=\"61\">dermis<\/span> profunda y la <span class=\"term\" data-term-id=\"1282\">subcutis<\/span> superficial [1].<\/p>\n<p>Esta condici\u00f3n tambi\u00e9n es referida en la literatura m\u00e9dica como arteritis linfoc\u00edtica macular.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Manifestaci\u00f3n Cut\u00e1nea: Livedo Racemosa<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/livedo4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsInkiLDg1XQ.jpg\" alt=\"Imagen representativa de livedo racemosa, caracterizada por un patr\u00f3n reticular viol\u00e1ceo en la piel.\">\n            <\/div>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2 id=\"quienes-padecen\">Perfil Demogr\u00e1fico de la Arteritis Trombof\u00edlica Linfoc\u00edtica<\/h2>\n<p>La arteritis linfoc\u00edtica trombof\u00edlica exhibe un predominio en el sexo femenino. La edad media de presentaci\u00f3n se sit\u00faa alrededor de los 39 a\u00f1os, con un rango amplio que abarca desde los 6 hasta los 73 a\u00f1os [2].<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2 id=\"causas\">Etiolog\u00eda de la Arteritis Trombof\u00edlica Linfoc\u00edtica<\/h2>\n<p>La causa precisa de la arteritis linfoc\u00edtica trombof\u00edlica a\u00fan no se ha determinado completamente. Se ha postulado que la endovasculitis linfoc\u00edtica subyacente desencadena una trombofilia <span class=\"term\" data-term-id=\"324\">localizada<\/span>. Esta trombofilia se evidencia histol\u00f3gicamente por la presencia de un anillo de <span class=\"term\" data-term-id=\"850\">fibrina<\/span> intraluminal, sin que exista destrucci\u00f3n demostrable de la pared del vaso [1].<\/p>\n<ul class=\"keyword-list\">\n<li>Ciertos casos han mostrado correlaci\u00f3n con <span class=\"term\" data-term-id=\"691\">autoinmune<\/span> <span class=\"term\" data-term-id=\"426\">anticuerpos<\/span> o la presencia de <span class=\"term\" data-term-id=\"1583\">heterocigosidad<\/span> para <span class=\"term\" data-term-id=\"871\">mutaciones<\/span> protromb\u00f3ticas, lo que insin\u00faa la posible contribuci\u00f3n de factores tanto autoinmunol\u00f3gicos como trombof\u00edlicos.<\/li>\n<li>Aunque se han detectado anticuerpos antifosfol\u00edpidos en algunas situaciones, los bajos <span class=\"term\" data-term-id=\"2289\">t\u00edtulos<\/span> observados y la ausencia de caracter\u00edsticas <span class=\"term\" data-term-id=\"380\">sist\u00e9micas<\/span> restan peso a la contribuci\u00f3n significativa del <span class=\"term\" data-term-id=\"350\">s\u00edndrome<\/span> antifosfol\u00edpido en su <span class=\"term\" data-term-id=\"527\">patog\u00e9nesis<\/span> [1,3].<\/li>\n<li>Se han reportado niveles bajos a moderados de anticuerpos antinucleares (ANA); no obstante, en dichos pacientes no se encontr\u00f3 evidencia de enfermedad del <span class=\"term\" data-term-id=\"43\">tejido conectivo<\/span> [1,4].<\/li>\n<\/ul>\n<h2 id=\"caracteristicas-clinicas\">Hallazgos Cl\u00ednicos de la Arteritis Trombof\u00edlica Linfoc\u00edtica<\/h2>\n<p>Las manifestaciones cl\u00ednicas t\u00edpicas de la arteritis trombof\u00edlica linfoc\u00edtica incluyen los siguientes elementos:<\/p>\n<ul>\n<li>Presentaci\u00f3n de livedo racemosa o hiperpigmentaci\u00f3n macular <span class=\"term\" data-term-id=\"2193\">persistente<\/span>, afectando primariamente las extremidades inferiores; si bien las extremidades superiores tambi\u00e9n pueden involucrarse, su afectaci\u00f3n es menor. Esta coloraci\u00f3n cut\u00e1nea no es <span class=\"term\" data-term-id=\"1173\">blanqueable<\/span> y puede configurar un patr\u00f3n <span class=\"term\" data-term-id=\"9\">anular<\/span>.<\/li>\n<\/ul>\n<\/section>\n<p>```<\/p>\n<p><span class=\"term\" data-term-id=\"1171\">Induraciones<\/span> <span class=\"term\" data-term-id=\"900\">subcut\u00e1neas<\/span> <span class=\"term\" data-term-id=\"1171\">palpables<\/span><\/p>\n<ul>\n<li>Algunos reportes indican presencia de <span class=\"term\" data-term-id=\"1278\">ulceraci\u00f3n<\/span> [5,6]<\/li>\n<li>Inexistencia de prurito o dolor<\/li>\n<li>Ausencia de <span class=\"term\" data-term-id=\"250\">p\u00farpura<\/span>, cicatrices o <span class=\"term\" data-term-id=\"17\">atrofia blanca<\/span>.<\/li>\n<\/ul>\n<h1>\u00bfC\u00f3mo se diagnostica la arteritis linfoc\u00edtica trombof\u00edlica?<\/h1>\n<p>El diagn\u00f3stico de arteritis trombof\u00edlica linfoc\u00edtica se establece mediante la correlaci\u00f3n de caracter\u00edsticas cl\u00ednicas distintivas con hallazgos histopatol\u00f3gicos espec\u00edficos. [1].<\/p>\n<ul>\n<li>Se observa un denso <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> <span class=\"term\" data-term-id=\"490\">inflamatorio<\/span> alojado en la pared de los vasos musculares. Este afecta primariamente a las arterias de calibre peque\u00f1o y mediano localizadas en la dermis profunda, la uni\u00f3n dermoepid\u00e9rmica y el tejido subcut\u00e1neo superficial.<\/li>\n<li>Dicho infiltrado inflamatorio se compone mayoritariamente de c\u00e9lulas mononucleares, con predominio de <span class=\"term\" data-term-id=\"421\">linfocitos<\/span> y una menor proporci\u00f3n de <span class=\"term\" data-term-id=\"858\">histiocitos<\/span>.<\/li>\n<li>Hay una escasez o ausencia total de <span class=\"term\" data-term-id=\"442\">neutr\u00f3filos<\/span> y <span class=\"term\" data-term-id=\"448\">eosin\u00f3filos<\/span>.<\/li>\n<li>Se identifica un anillo de fibrina <span class=\"term\" data-term-id=\"1341\">hialinizado<\/span> y <span class=\"term\" data-term-id=\"2002\">conc\u00e9ntrico<\/span> que envuelve completamente la <span class=\"term\" data-term-id=\"2120\">lumen<\/span> de los vasos afectados.<\/li>\n<\/ul>\n<p>Es crucial destacar que no se presentan signos ni s\u00edntomas de vasculitis sist\u00e9mica (consultar sobre la <span class=\"term\" data-term-id=\"47\">vasculitis cut\u00e1nea<\/span>) [2].<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                        <!-- \/340621630\/dermnet_mobile_after4sections_300x250' --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-9\" class=\"[ js-hideable ]\"><\/div>\n<p><script>\n    if (ads_screenwidth < 780 ) {\n        var inline = document.createElement(\"div\");\n        var ad = document.createElement(\"div\");\n\n        ad.id = 'div-gpt-ad-1484122037505-9';\n        ad.style.height=\"250px\";\n        ad.style.width=\"300px;\";\n\n        inline.appendChild(ad);\n        inline.className = \"inline\";\n        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-9\");\n        placeholder.parentNode.replaceChild(inline, placeholder);\n        (function () {\n            googletag.cmd.push(function () {\n                googletag.display('div-gpt-ad-1484122037505-9');\n            });\n        })();\n    }\n<\/script>\n                    <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>\u00bfCu\u00e1l es el <span class=\"term\" data-term-id=\"813\">diagn\u00f3stico diferencial<\/span> de la arteritis trombof\u00edlica linfoc\u00edtica?<\/h2>\n<p>Es fundamental diferenciar la arteritis trombof\u00edlica linfoc\u00edtica de otras afecciones <span class=\"term\" data-term-id=\"878\">oclusivas<\/span> <span class=\"term\" data-term-id=\"753\">vasculares<\/span> que tambi\u00e9n presentan livedo reticularis como manifestaci\u00f3n cl\u00ednica.<\/p>\n<h3>Poliarteritis nudosa cut\u00e1nea<\/h3>\n<ul>\n<li>La poliarteritis nudosa cut\u00e1nea se distingue por la aparici\u00f3n de <span class=\"term\" data-term-id=\"367\">n\u00f3dulos<\/span> subcut\u00e1neos dolorosos y ulceraciones, caracter\u00edsticas que son poco comunes en la arteritis trombof\u00edlica linfoc\u00edtica [7].<\/li>\n<li>En la poliarteritis nudosa cut\u00e1nea, el livedo se circunscribe a la zona circundante a las <span class=\"term\" data-term-id=\"1279\">\u00falceras<\/span>, adoptando un patr\u00f3n estrellado y de contornos irregulares [7].<\/li>\n<li>En fases tempranas, la poliarteritis nudosa cut\u00e1nea muestra una <span class=\"term\" data-term-id=\"543\">infiltraci\u00f3n<\/span> <span class=\"term\" data-term-id=\"443\">neutrof\u00edlica<\/span> que afecta la capa muscular de las arterias peque\u00f1as y medianas; en etapas posteriores es m\u00e1s notoria la participaci\u00f3n de c\u00e9lulas mononucleares [7].<\/li>\n<\/ul>\n<h3><span class=\"term\" data-term-id=\"1350\">Vasculopat\u00eda<\/span> <span class=\"term\" data-term-id=\"595\">Livedoide<\/span><\/h3>\n<ul>\n<li>Si bien puede estar presente el livedo racemosa, la vasculopat\u00eda livedoide t\u00edpicamente se manifiesta inicialmente con episodios de p\u00farpura y ulceraci\u00f3n dolorosa en las extremidades inferiores, culminando en atrofia blanca.<\/li>\n<li>Existe <span class=\"term\" data-term-id=\"370\">deposici\u00f3n<\/span> de fibrina luminal en la vasculopat\u00eda livedoide, pero el infiltrado inflamatorio tiende a ser escaso [1,8].<\/li>\n<\/ul>\n<h3>S\u00edndrome antifosfol\u00edpido<\/h3>\n<ul>\n<li>El livedo racemosa tambi\u00e9n puede observarse en el contexto del s\u00edndrome antifosfol\u00edpido.<\/li>\n<li>En este s\u00edndrome, predominan los fen\u00f3menos de <span class=\"term\" data-term-id=\"769\">trombosis<\/span> sin evidencia de <span class=\"term\" data-term-id=\"148\">inflamaci\u00f3n<\/span> significativa en la pared del vaso.<\/li>\n<li>El s\u00edndrome antifosfol\u00edpido se caracteriza por<\/li>\n<\/ul>\n<p>Para finalizar, comprender estas diferencias morfol\u00f3gicas y cl\u00ednicas es esencial para asegurar un diagn\u00f3stico preciso de la arteritis linfoc\u00edtica trombof\u00edlica y diferenciarla de otras vasculopat\u00edas cut\u00e1neas que comparten la caracter\u00edstica del livedo reticularis.<\/p>\n<ul>\n<li><span class=\"term\" data-term-id=\"805\">Trombosis recurrente<\/span>, abortos espont\u00e1neos y <span class=\"term\" data-term-id=\"623\">trombocitopenia<\/span> [9].<\/li>\n<\/ul>\n<section>\n<h2>S\u00edndrome de Sneddon<\/h2>\n<ul>\n<li>El patr\u00f3n de livedo racemosa en el s\u00edndrome de Sneddon es m\u00e1s extenso en comparaci\u00f3n con la arteritis trombof\u00edlica linfoc\u00edtica [3].<\/li>\n<li>El livedo es m\u00e1s <span class=\"term\" data-term-id=\"242\">proximal<\/span> en el s\u00edndrome de Sneddon, afectando el tronco y la espalda; las extremidades rara vez se ven comprometidas.<\/li>\n<li>El diagn\u00f3stico del s\u00edndrome de Sneddon exige una intervenci\u00f3n <span class=\"term\" data-term-id=\"1848\">cerebrovascular<\/span> [10].<\/li>\n<\/ul>\n<\/section>\n<section>\n<h2>Tratamiento para la Arteritis Trombof\u00edlica Linfoc\u00edtica<\/h2>\n<p>La arteritis linfoc\u00edtica trombof\u00edlica generalmente presenta un curso <span class=\"term\" data-term-id=\"1532\">indolente<\/span>, caracterizado por livedo racemosa persistente o hiperpigmentaci\u00f3n macular <span class=\"term\" data-term-id=\"731\">asintom\u00e1tica<\/span> [1]. Dado que la mayor\u00eda de las <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> no causan s\u00edntomas, el tratamiento no siempre es necesario [2].<\/p>\n<p>Las siguientes opciones terap\u00e9uticas han demostrado ser beneficiosas:<\/p>\n<ul>\n<li>Aspirina<\/li>\n<li>Pentoxifilina<\/li>\n<li>Dapsona<\/li>\n<\/ul>\n<p>El uso de esteroides orales y <span class=\"term\" data-term-id=\"1330\">t\u00f3picos<\/span> no ha demostrado ser efectivo [2].<\/p>\n<p>Debido a la rareza de la arteritis trombof\u00edlica linfoc\u00edtica y las respuestas inconsistentes al tratamiento, actualmente no existe un consenso claro sobre las recomendaciones terap\u00e9uticas espec\u00edficas.<\/p>\n<\/section>\n<section>\n<h2>Pron\u00f3stico de la Arteritis Trombof\u00edlica Linfoc\u00edtica<\/h2>\n<p>La arteritis linfoc\u00edtica trombof\u00edlica tiende a seguir un curso <span class=\"term\" data-term-id=\"319\">cr\u00f3nico<\/span> e indolente, sin progresar a vasculitis sist\u00e9mica en la mayor\u00eda de los casos [1,2]. Se recomienda un seguimiento continuo, ya que se han reportado casos raros de desarrollo posterior de vasculitis sist\u00e9mica [11]. El <span class=\"term\" data-term-id=\"241\">pron\u00f3stico<\/span> a largo plazo todav\u00eda no est\u00e1 completamente establecido.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>\u00ab`html Arteritis Linfoc\u00edtica Trombof\u00edlica: Definici\u00f3n, Causas y Presentaci\u00f3n Cl\u00ednica Definici\u00f3n de Arteritis Linfoc\u00edtica Trombof\u00edlica La arteritis linfoc\u00edtica trombof\u00edlica se clasifica como una primaria vasculitis linfoc\u00edtica. Cl\u00ednicamente, se manifiesta a trav\u00e9s de livedo racemosa o macular hiperpigmentaci\u00f3n. Histol\u00f3gicamente, presenta hallazgos distintivos que afectan a las arterias peque\u00f1as y medianas localizadas en la dermis profunda y la [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":13434,"parent":0,"template":"","glossary-cat":[],"class_list":["post-13432","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Arteritis linfoc\u00edtica trombof\u00edlica - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/de\/lymphozytisch-thrombophile-arteriitis\/\" \/>\n<meta property=\"og:locale\" content=\"de_DE\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Arteritis linfoc\u00edtica trombof\u00edlica\" \/>\n<meta property=\"og:description\" content=\"\u00ab`html Arteritis Linfoc\u00edtica Trombof\u00edlica: Definici\u00f3n, Causas y Presentaci\u00f3n Cl\u00ednica Definici\u00f3n de Arteritis Linfoc\u00edtica Trombof\u00edlica La arteritis linfoc\u00edtica trombof\u00edlica se clasifica como una primaria vasculitis linfoc\u00edtica. Cl\u00ednicamente, se manifiesta a trav\u00e9s de livedo racemosa o macular hiperpigmentaci\u00f3n. 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