{"id":12209,"date":"2020-11-19T08:58:16","date_gmt":"2020-11-19T08:58:16","guid":{"rendered":"https:\/\/dermatly.com\/patologia-inflamatoria-del-tumor-miofibroblastico\/"},"modified":"2026-03-10T16:57:09","modified_gmt":"2026-03-10T16:57:09","slug":"entzundungspathologie-des-myofibroblastischen-tumors","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/de\/patologia-inflamatoria-del-tumor-miofibroblastico\/","title":{"rendered":"Inflammatorische Myofibroblastische Pathologie"},"content":{"rendered":"<section class=\"textBlock\">\n<h1>Tumor Miofibrobl\u00e1stico Inflamatorio: Caracter\u00edsticas y Diagn\u00f3stico Dermatol\u00f3gico<\/h1>\n<p>El <span class=\"term\" data-term-id=\"490\">tumor<\/span> <span class=\"term\" data-term-id=\"490\">inflamatorio<\/span> miofibrobl\u00e1stico (IMT) raramente se manifiesta en la piel como una lesi\u00f3n <span class=\"term\" data-term-id=\"52\">d\u00e9rmica<\/span>. Una caracter\u00edstica clave en muchos de estos tumores es la presencia de una <span class=\"term\" data-term-id=\"1849\">translocaci\u00f3n<\/span> del <span class=\"term\" data-term-id=\"774\">gen<\/span> <em>ALK<\/em>. Hist\u00f3ricamente, algunas variantes de esta afecci\u00f3n fueron inapropiadamente clasificadas como &#8216;pseudotumores&#8217; o &#8216;<span class=\"term\" data-term-id=\"1513\">granulomas<\/span> de <span class=\"term\" data-term-id=\"1536\">c\u00e9lulas<\/span> plasm\u00e1ticas&#8217;.<\/p>\n<h2>Histolog\u00eda Caracter\u00edstica del Tumor Miofibrobl\u00e1stico Inflamatorio<\/h2>\n<p><span class=\"term\" data-term-id=\"1669\">Histol\u00f3gicamente<\/span>, la <span class=\"term\" data-term-id=\"164\">lesi\u00f3n<\/span> se localiza predominantemente en la <span class=\"term\" data-term-id=\"61\">dermis<\/span>, extendi\u00e9ndose bajo un <span class=\"term\" data-term-id=\"85\">epidermis<\/span> de apariencia normal (Figura 1). El tumor se compone de una mezcla heterog\u00e9nea de c\u00e9lulas fusiformes y ovoides, acompa\u00f1adas de un prominente <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> inflamatorio (figuras 2-3). Es importante destacar que este infiltrado es t\u00edpicamente rico en <span class=\"term\" data-term-id=\"2209\">C\u00e9lulas plasm\u00e1ticas<\/span> (observables claramente en la Figura 2). Dependiendo del caso, pueden observarse cierto grado de <span class=\"term\" data-term-id=\"1539\">pleomorfismo<\/span> celular y figuras <span style=\"font-style: italic;\">mit\u00f3ticas<\/span> ocasionales (vista se\u00f1alada por la flecha en la figura 3).<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Evaluaci\u00f3n Patol\u00f3gica del Tumor Miofibrobl\u00e1stico Inflamatorio<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<figure>\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/figure-1-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Imagen histopatol\u00f3gica que muestra la lesi\u00f3n d\u00e9rmica del tumor miofibrobl\u00e1stico inflamatorio.\">\n                <\/div><figcaption class=\"p-small\">Figura 1<\/figcaption><\/figure>\n<figure>\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/Figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Imagen histopatol\u00f3gica que muestra el infiltrado inflamatorio rico en c\u00e9lulas plasm\u00e1ticas, caracter\u00edstico del IMT.\">\n                <\/div><figcaption class=\"p-small\">Figura 2<\/figcaption><\/figure>\n<figure>\n<div class=\"imageLinkBlock__item__image\">\n                    <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/Figure-4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microfotograf\u00eda que ilustra el pleomorfismo celular y figuras mit\u00f3ticas (flecha) dentro de las c\u00e9lulas tumorales del IMT.\">\n                <\/div><figcaption class=\"p-small\">figura 3<\/figcaption><\/figure>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth < 780 ) {\n                        var inline = document.createElement(\"div\");\n                        var ad = document.createElement(\"div\");\n\n                        ad.id = 'div-gpt-ad-1484122037505-8';\n                        ad.style.height=\"250px\";\n                        ad.style.width=\"300px;\";\n\n                        inline.appendChild(ad);\n                        inline.className = \"inline\";\n                        var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n                        placeholder.parentNode.replaceChild(inline, placeholder);\n                        (function () {\n                            googletag.cmd.push(function () {\n                                googletag.display('div-gpt-ad-1484122037505-8');\n                            });\n                        })();\n                    }\n                <\/script>\n            <\/div>\n<\/p><\/div>\n<\/p><\/div>\n<h2>Tinciones Especiales para el Diagn\u00f3stico del Tumor Miofibrobl\u00e1stico Inflamatorio<\/h2>\n<p>En el an\u00e1lisis inmunohistoqu\u00edmico, las c\u00e9lulas tumorales muestran una fuerte tinci\u00f3n positiva para vimentina y marcadores de m\u00fasculo liso de manera variable. La AME (Alfa-1-antitripsina) resulta positiva en hasta un 90% de los casos. La detecci\u00f3n de ALK (<span class=\"term\" data-term-id=\"1327\">linfoma<\/span> quinasa <span class=\"term\" data-term-id=\"976\">anapl\u00e1sico<\/span>) mediante <span class=\"term\" data-term-id=\"1421\">inmunohistoqu\u00edmica<\/span> es crucial, ya que su positividad es pr\u00e1cticamente diagn\u00f3stica cuando se observa en el contexto cl\u00ednico y morfol\u00f3gico adecuado. Adicionalmente, las pruebas gen\u00e9ticas como FISH pueden emplearse para detectar reordenamientos del gen ALK.<\/p>\n<h2>Consideraciones en el Diagn\u00f3stico Diferencial de Patolog\u00eda del IMT<\/h2>\n<p>El diagn\u00f3stico diferencial del IMT debe incluir varios tumores mesenquimales de car\u00e1cter inflamatorio; espec\u00edficamente, <span class=\"term\" data-term-id=\"1540\">sarcomas<\/span> <span class=\"term\" data-term-id=\"1666\">pleom\u00f3rficos<\/span>, <span class=\"term\" data-term-id=\"1670\">melanoma<\/span> y <span class=\"term\" data-term-id=\"1673\">leiomiosarcoma<\/span>, ya que todos pueden presentar variantes con marcadas caracter\u00edsticas inflamatorias. La evaluaci\u00f3n de la positividad de ALK mediante tinci\u00f3n inmunohistoqu\u00edmica o FISH resulta fundamental para resolver casos histol\u00f3gicamente complicados.<\/p>\n<p>En cuanto al pseudotumor y el granuloma de <span class=\"term\" data-term-id=\"2208\">c\u00e9lulas plasm\u00e1ticas<\/span>, estos se distinguen por la marcada ausencia de <span class=\"term\" data-term-id=\"1305\">atipia<\/span> notable y, crucialmente, carecen de las <span class=\"term\" data-term-id=\"1850\">translocaciones<\/span> del <span class=\"term\" data-term-id=\"774\">gen<\/span> <em>ALK<\/em>. Es importante reconocer que muchos casos hoy clasificados como IMT fueron clasificados err\u00f3neamente como pseudotumores en el pasado.<\/p>\n<\/section>\n","protected":false},"excerpt":{"rendered":"<p>Tumor Miofibrobl\u00e1stico Inflamatorio: Caracter\u00edsticas y Diagn\u00f3stico Dermatol\u00f3gico El tumor inflamatorio miofibrobl\u00e1stico (IMT) raramente se manifiesta en la piel como una lesi\u00f3n d\u00e9rmica. Una caracter\u00edstica clave en muchos de estos tumores es la presencia de una translocaci\u00f3n del gen ALK. Hist\u00f3ricamente, algunas variantes de esta afecci\u00f3n fueron inapropiadamente clasificadas como &#8216;pseudotumores&#8217; o &#8216;granulomas de c\u00e9lulas plasm\u00e1ticas&#8217;. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":12213,"parent":0,"template":"","glossary-cat":[],"class_list":["post-12209","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda inflamatoria del tumor miofibrobl\u00e1stico - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/de\/entzundungspathologie-des-myofibroblastischen-tumors\/\" \/>\n<meta property=\"og:locale\" content=\"de_DE\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda inflamatoria del tumor miofibrobl\u00e1stico\" \/>\n<meta property=\"og:description\" content=\"Tumor Miofibrobl\u00e1stico Inflamatorio: Caracter\u00edsticas y Diagn\u00f3stico Dermatol\u00f3gico El tumor inflamatorio miofibrobl\u00e1stico (IMT) raramente se manifiesta en la piel como una lesi\u00f3n d\u00e9rmica. Una caracter\u00edstica clave en muchos de estos tumores es la presencia de una translocaci\u00f3n del gen ALK. Hist\u00f3ricamente, algunas variantes de esta afecci\u00f3n fueron inapropiadamente clasificadas como &#8216;pseudotumores&#8217; o &#8216;granulomas de c\u00e9lulas plasm\u00e1ticas&#8217;. 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