{"id":11435,"date":"2020-11-18T19:19:47","date_gmt":"2020-11-18T19:19:47","guid":{"rendered":"https:\/\/dermatly.com\/patologia-de-la-hidroa-vacciniforme\/"},"modified":"2026-03-10T16:35:47","modified_gmt":"2026-03-10T16:35:47","slug":"pathologie-der-vacciniform-hydroa","status":"publish","type":"glossary","link":"https:\/\/dermatly.com\/de\/patologia-de-la-hidroa-vacciniforme\/","title":{"rendered":"Patolog\u00eda de la hidroa vacciniforme"},"content":{"rendered":"<section class=\"textBlock\">\n<p>La hidroa vacciniforme es una fotodermatosis infrecuente, caracterizada t\u00edpicamente en la infancia por la aparici\u00f3n de <span class=\"term\" data-term-id=\"1028\">ves\u00edculas<\/span> que evolucionan a cicatrices. Aunque su <span class=\"term\" data-term-id=\"527\">patog\u00e9nesis<\/span> es poco comprendida, el virus de Epstein Barr (VEB) frecuentemente se identifica en el <span class=\"term\" data-term-id=\"541\">infiltrado<\/span> <span class=\"term\" data-term-id=\"52\">d\u00e9rmico<\/span>. Actualmente, existe debate sobre si el linfoma de <span class=\"term\" data-term-id=\"416\">c\u00e9lula T<\/span> tipo hidroa vacciniforme constituye una entidad <span class=\"term\" data-term-id=\"66\">discreta<\/span> o representa la manifestaci\u00f3n m\u00e1s grave dentro del espectro de la hidroa vacciniforme.<\/p>\n<h2>Histopatolog\u00eda de la Hidroa Vacciniforme<\/h2>\n<p>En los casos de hidroa vacciniforme, los cortes histol\u00f3gicos revelan <span class=\"term\" data-term-id=\"269\">espongiosis<\/span> <span class=\"term\" data-term-id=\"846\">epid\u00e9rmica<\/span>, <span class=\"term\" data-term-id=\"2428\">vesiculaci\u00f3n<\/span> y focal <span class=\"term\" data-term-id=\"403\">necrosis<\/span>. Estas alteraciones coexisten con un infiltrado d\u00e9rmico denso (Figura 1). Esta necrosis puede volverse <span class=\"term\" data-term-id=\"544\">confluente<\/span> (Figuras 2 y 3), y el infiltrado est\u00e1 compuesto por una mezcla de c\u00e9lulas <span class=\"term\" data-term-id=\"349\">agudas<\/span> y <span class=\"term\" data-term-id=\"319\">cr\u00f3nicas<\/span> <span class=\"term\" data-term-id=\"490\">inflamatorias<\/span>. Las <span class=\"term\" data-term-id=\"2115\">lesiones<\/span> m\u00e1s evolucionadas pueden mostrar evidencia de cicatrizaci\u00f3n.<\/p>\n<p>La Figura 4 ilustra el infiltrado m\u00e1s marcado que se observa en el linfoma de c\u00e9lulas T tipo hidroa vacciniforme, una condici\u00f3n que puede presentar cambios epid\u00e9rmicos y superficiales indistinguibles de la forma benigna.<\/p>\n<section class=\"textBlock imageLinkBlockTitle\">\n<h3 class=\"colour--primary\">Patolog\u00eda de la Hidroa Vacciniforme<\/h3>\n<\/section>\n<section class=\"imageLinkBlock\">\n<div class=\"flex\">\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/hydroa-vacciniforme-figure-1__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Microscop\u00eda de la hidroa vacciniforme mostrando Espongiosis epid\u00e9rmica\"><\/p>\n<p class=\"p-small\">Figura 1<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/hydroa-vacciniforme-figure-2__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Lesi\u00f3n de hidroa vacciniforme con necrosis confluente\"><\/p>\n<p class=\"p-small\">Figura 2<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/hydroa-vacciniforme-figure-3__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Detalle de necrosis confluente en hidroa vacciniforme\"><\/p>\n<p class=\"p-small\">Figura 3<\/p>\n<\/p><\/div>\n<div class=\"imageLinkBlock__item__image\">\n                <img decoding=\"async\" src=\"https:\/\/dermatly.com\/wp-content\/uploads\/2020\/11\/hydroa-vacciniforme-figure-4__ProtectWyJQcm90ZWN0Il0_FocusFillWzI5NCwyMjIsIngiLDFd.jpg\" alt=\"Infiltrado d\u00e9rmico denso caracter\u00edstico del linfoma de c\u00e9lulas T tipo hidroa vacciniforme\"><\/p>\n<p class=\"p-small\">Figura 4<\/p>\n<\/p><\/div>\n<\/p><\/div>\n<\/section>\n<div class=\"clearfix imageLinkBlock\"><\/div>\n<h2>Estudios Especiales para Diagnosticar Hidroa Vacciniforme<\/h2>\n<p>Para confirmar la presencia del agente etiol\u00f3gico, el VEB puede ser detectado en el infiltrado d\u00e9rmico utilizando t\u00e9cnicas espec\u00edficas, como la hibridaci\u00f3n in situ para <span class=\"term\" data-term-id=\"1077\">BORDE<\/span> (EBER).<\/p>\n<div id=\"square-placement-country-holder\" class=\"country-dependent advert\">\n<div class=\"box-placement square-placement\">\n<div class=\"advert__frame\">\n                <!-- \/340621630\/dermnet_mobile_afterfirstsection_300x250 --><\/p>\n<div style=\"display: none;\" id=\"hidden-div-gpt-ad-1484122037505-8\" class=\"[ js-hideable ]\"><\/div>\n<p>                <script>\n                    if (ads_screenwidth\n<\/section>\n<div class=\"js-ad-container\">\n    <script>\n        if (window.innerWidth < 780) {\n            var inline = document.createElement(\"div\");\n            var ad = document.createElement(\"div\");\n\n            ad.id = 'div-gpt-ad-1484122037505-8';\n            ad.style.height = \"250px\";\n            ad.style.width = \"300px;\";\n\n            inline.appendChild(ad);\n            inline.className = \"inline\";\n            var placeholder = document.getElementById(\"hidden-div-gpt-ad-1484122037505-8\");\n            placeholder.parentNode.replaceChild(inline, placeholder);\n            (function() {\n                googletag.cmd.push(function() {\n                    googletag.display('div-gpt-ad-1484122037505-8');\n                });\n            })();\n        }\n    <\/script>\n<\/div>\n<p><main><\/p>\n<section>\n<h1>Diagn\u00f3stico Diferencial de la Hidroa Vacciniforme<\/h1>\n<p>Establecer el diagn\u00f3stico diferencial preciso de la hidroa vacciniforme (HV) es crucial para diferenciarla de otras afecciones cut\u00e1neas que presentan lesiones similares. Una entidad que requiere cuidadosa consideraci\u00f3n es el Linfoma de C\u00e9lulas T similar a la Hidroa Vacciniforme.<\/p>\n<p>Actualmente, la relaci\u00f3n entre estos dos diagn\u00f3sticos\u2014si se trata de una entidad separada o si el linfoma se sit\u00faa dentro del espectro de la HV\u2014a\u00fan se est\u00e1 debatiendo. No obstante, el linfoma asociado a HV frecuentemente presenta caracter\u00edsticas distintivas. Las lesiones tienden a ser de mayor tama\u00f1o, muestran una menor propensi\u00f3n a la resoluci\u00f3n espont\u00e1nea y pueden manifestarse en sitios anat\u00f3micos no expuestos habitualmente a la radiaci\u00f3n solar.<\/p>\n<p>Histopatol\u00f3gicamente, el infiltrado en la <span class=\"term\" data-term-id=\"61\">dermis<\/span> puede ser notablemente m\u00e1s denso en comparaci\u00f3n con la HV cl\u00e1sica. Adem\u00e1s, existe la posibilidad de que la grasa <span class=\"term\" data-term-id=\"900\">subcut\u00e1nea<\/span> tambi\u00e9n se encuentre infiltrada (figura 4). Los an\u00e1lisis inmunohistoqu\u00edmicos son fundamentales, ya que revelan com\u00fanmente un infiltrado predominantemente compuesto por <span class=\"term\" data-term-id=\"417\">c\u00e9lulas T<\/span> (CD3+, CD8+, TIA+) o <span class=\"term\" data-term-id=\"584\">c\u00e9lulas NK<\/span> (CD56+). Adem\u00e1s, los estudios de reordenamiento del <span class=\"term\" data-term-id=\"774\">gen<\/span> pueden arrojar resultados positivos, y la hibridaci\u00f3n in situ para detectar el virus de Epstein-Barr (EBV) puede ser positiva dentro del infiltrado celular.<\/p>\n<\/section>\n<p><\/main><\/p>\n","protected":false},"excerpt":{"rendered":"<p>La hidroa vacciniforme es una fotodermatosis infrecuente, caracterizada t\u00edpicamente en la infancia por la aparici\u00f3n de ves\u00edculas que evolucionan a cicatrices. Aunque su patog\u00e9nesis es poco comprendida, el virus de Epstein Barr (VEB) frecuentemente se identifica en el infiltrado d\u00e9rmico. Actualmente, existe debate sobre si el linfoma de c\u00e9lula T tipo hidroa vacciniforme constituye una [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":11440,"parent":0,"template":"","glossary-cat":[],"class_list":["post-11435","glossary","type-glossary","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.2 (Yoast SEO v27.1.1) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Patolog\u00eda de la hidroa vacciniforme - Dermatly.com - El sitio de tu piel<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/dermatly.com\/de\/pathologie-der-vacciniform-hydroa\/\" \/>\n<meta property=\"og:locale\" content=\"de_DE\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Patolog\u00eda de la hidroa vacciniforme\" \/>\n<meta property=\"og:description\" content=\"La hidroa vacciniforme es una fotodermatosis infrecuente, caracterizada t\u00edpicamente en la infancia por la aparici\u00f3n de ves\u00edculas que evolucionan a cicatrices. 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